Publications

Outcomes of Infants and Young Children With Relapsed Medulloblastoma After Initial Craniospinal Irradiation–Sparing Approaches: An International Cohort Study
Journal of Clinical Oncology
Craig Erker and Martin Mynarek and Simon Bailey and Claire M. Mazewski and Lorena Baroni and Maura Massimino and Juliette Hukin and Dolly Aguilera and Andrea M. Cappellano and Vijay Ramaswamy and Alvaro Lassaletta and Sébastien Perreault and Cassie N. Kline and Revathi Rajagopal and George Michaiel and Michal Zapotocky and Vicente Santa-Maria Lopez and Andres Morales La Madrid and Chantel Cacciotti and Eric S. Sandler and Lindsey M. Hoffman and Darren Klawinski and Sara Khan and Ralph Salloum and Anna L. Hoppmann and Valérie Larouche and Kathleen Dorris and Helen Toledano and Stephen W. Gilheeney and Mohamed S. Abdelbaki and Beverly Wilson and Derek S. Tsang and Jeffrey Knipstein and Michal Yalon Oren and Shafqat Shah and Jeffrey C. Murray and Kevin F. Ginn and Zhihong J. Wang and Gudrun Fleischhack and Denise Obrecht and Svenja Tonn and Virginia L. Harrod and Kara Matheson and Bruce Crooks and Douglas R. Strother and Kenneth J. Cohen and Jordan R. Hansford and Sabine Mueller and Ashle
DOI: 10.1200/JCO.21.02968
04/2023

Low-grade diffusely infiltrative tumour (LGDIT), SMARCB1-mutant: A clinical and histopathological distinct entity showing epigenetic similarity with ATRT-MYC
Neuropathology and Applied Neurobiology
Hasselblatt, M. and Thomas, C. and Federico, A. and Bens, S. and Hellström, M. and Casar-Borota, O. and Kordes, U. and Neumann, J.E. and Dottermusch, M. and Rodriguez, F.J. and Lo, A.C. and Cheng, S. and Hendson, G. and Hukin, J. and Hartmann, C. and Koch, A. and Capper, D. and Siebert, R. and Paulus, W. and Nemes, K. and Johann, P.D. and Frühwald, M.C. and Kool, M.
DOI: 10.1111/nan.12797
2022

Treatment-responsive Holmes tremor in a child with low-pressure hydrocephalus: video case report and systematic review of the literature
Journal of Neurosurgery: Pediatrics
Chang, S.J. and Mitchell, R. and Hukin, J. and Singhal, A.
DOI: 10.3171/2021.12.PEDS21539
2022

A case series of pediatric survivors of anaplastic pleomorphic xanthoastrocytoma
Neuro-Oncology Advances
Rebecca Ronsley and Christopher Dunham and Stephen Yip and Lindsay Brown and Jeffrey A Zuccato and Shirin Karimi and Gelareh Zadeh and Karen Goddard and Ash Singhal and Juliette Hukin and Sylvia Cheng
DOI: 10.1093/noajnl/vdaa176
01/2021

Trametinib therapy for children with neurofibromatosis type 1 and life-threatening plexiform neurofibroma or treatment-refractory low-grade glioma
Cancer Medicine
Ronsley, R. and Hounjet, C.D. and Cheng, S. and Rassekh, S.R. and Duncan, W.J. and Dunham, C. and Gardiner, J. and Ghag, A. and Ludemann, J.P. and Wensley, D. and Rehmus, W. and Sargent, M.A. and Hukin, J.
DOI: 10.1002/cam4.3910
2021

Multi-institutional analysis of treatment modalities in basal ganglia and thalamic germinoma
Pediatric Blood and Cancer
Graham, R.T. and Abu-Arja, M.H. and Stanek, J.R. and Cappellano, A. and Coleman, C. and Chi, S. and Cooney, T. and Dhall, G. and Ellen, J.G. and Finlay, J.L. and Fisher, M.J. and Friedman, G.K. and Gajjar, A. and Gauvain, K. and Hoffman, L.M. and Hukin, J. and Lucas, J.T. and Mueller, S. and Navalkele, P. and Ronsley, R. and Tinkle, C. and Villeneuve, S. and Yeo, K.K. and Su, J.M. and Margol, A. and Gottardo, N.G. and Allen, J. and Packer, R. and Bartels, U. and Abdelbaki, M.S.
DOI: 10.1002/pbc.29172
2021

Clinical Outcomes and Patient-Matched Molecular Composition of Relapsed Medulloblastoma
Journal of Clinical Oncology
Kumar, R. and Smith, K.S. and Deng, M. and Terhune, C. and Robinson, G.W. and Orr, B.A. and Liu, A.P.Y. and Lin, T. and Billups, C.A. and Chintagumpala, M. and Bowers, D.C. and Hassall, T.E. and Hansford, J.R. and Khuong-Quang, D.A. and Crawford, J.R. and Bendel, A.E. and Gururangan, S. and Schroeder, K. and Bouffet, E. and Bartels, U. and Fisher, M.J. and Cohn, R. and Partap, S. and Kellie, S.J. and McCowage, G. and Paulino, A.C. and Rutkowski, S. and Fleischhack, G. and Dhall, G. and Klesse, L.J. and Leary, S. and Nazarian, J. and Kool, M. and Wesseling, P. and Ryzhova, M. and Zheludkova, O. and Golanov, A.V. and McLendon, R.E. and Packer, R.J. and Dunham, C. and Hukin, J. and Fouladi, M. and Faria, C.C. and Pimentel, J. and Walter, A.W. and Jabado, N. and Cho, Y.-J. and Perreault, S. and Croul, S.E. and Zapotocky, M. and Hawkins, C. and Tabori, U. and Taylor, M.D. and Pfister, S.M. and Klimo, P. and Boop, F.A. and Ellison, D.W. and Merchant, T.E. and Onar-Thomas, A. and Korshunov, A. and Jones, D.T.W. and Gajjar, A. and Ramaswamy, V. and Northcott, P.A.
DOI: 10.1200/JCO.20.01359
2021

Histologic Correlates of Molecular Group 4 Pediatric Medulloblastoma: A Retrospective Canadian Review
Pediatric and Developmental Pathology
Triscott, J. and Yip, S. and Johnston, D. and Michaud, J. and Rassekh, S.R. and Hukin, J. and Dunn, S. and Dunham, C.
DOI: 10.1177/10935266211001986
2021

Author Correction: Locoregional delivery of CAR T cells to the cerebrospinal fluid for treatment of metastatic medulloblastoma and ependymoma (Nature Medicine, (2020), 26, 5, (720-731), 10.1038/s41591-020-0827-2)
Nature Medicine
Donovan, L.K. and Delaidelli, A. and Joseph, S.K. and Bielamowicz, K. and Fousek, K. and Holgado, B.L. and Manno, A. and Srikanthan, D. and Gad, A.Z. and Van Ommeren, R. and Przelicki, D. and Richman, C. and Ramaswamy, V. and Daniels, C. and Pallota, J.G. and Douglas, T. and Joynt, A.C.M. and Haapasalo, J. and Nor, C. and Vladoiu, M.C. and Kuzan-Fischer, C.M. and Garzia, L. and Mack, S.C. and Varadharajan, S. and Baker, M.L. and Hendrikse, L. and Ly, M. and Kharas, K. and Balin, P. and Wu, X. and Qin, L. and Huang, N. and Stucklin, A.G. and Morrissy, A.S. and Cavalli, F.M.G. and Luu, B. and Suarez, R. and De Antonellis, P. and Michealraj, A. and Rastan, A. and Hegde, M. and Komosa, M. and Sirbu, O. and Kumar, S.A. and Abdullaev, Z. and Faria, C.C. and Yip, S. and Hukin, J. and Tabori, U. and Hawkins, C. and Aldape, K. and Daugaard, M. and Maris, J.M. and Sorensen, P.H. and Ahmed, N. and Taylor, M.D.
DOI: 10.1038/s41591-021-01362-1
2021

Targeting integrated epigenetic and metabolic pathways in lethal childhood PFA ependymomas
Science Translational Medicine
Panwalkar, P. and Tamrazi, B. and Dang, D. and Chung, C. and Sweha, S. and Natarajan, S.K. and Pun, M. and Bayliss, J. and Ogrodzinski, M.P. and Pratt, D. and Mullan, B. and Hawes, D. and Yang, F. and Lu, C. and Sabari, B.R. and Achreja, A. and Heon, J. and Animasahun, O. and Cieslik, M. and Dunham, C. and Yip, S. and Hukin, J. and Phillips, J.J. and Bornhorst, M. and Griesinger, A.M. and Donson, A.M. and Foreman, N.K. and Garton, H.J.L. and Heth, J. and Muraszko, K. and Nazarian, J. and Koschmann, C. and Jiang, L. and Filbin, M.G. and Nagrath, D. and Kool, M. and Korshunov, A. and Pfister, S.M. and Gilbertson, R.J. and David Allis, C. and Chinnaiyan, A.M. and Lunt, S.Y. and Blüml, S. and Judkins, A.R. and Venneti, S.
DOI: 10.1126/scitranslmed.abc0497
2021

Factors influencing cognitive outcome in opsoclonus–myoclonus syndrome
Developmental Medicine & Child Neurology
Juliette Hukin
DOI: 10.1111/dmcn.14669
12/2020

MBCL-24. CAN YOUNG CHILDREN WITH RELAPSED MEDULLOBLASTOMA BE SALVAGED AFTER INITIAL IRRADIATION-SPARING APPROACHES?
Neuro-oncology
Erker C and Larouche V and Margol A and Cacciotti C and Perreault S and Cohen K and AbdelBaki M and Hukin J and Rassekh S and Eisenstat D and Wilson B and Knipstein J and Hoppmann A and Lafay-Cousin L
12/2020

GCT-23. MULTI-INSTITUTIONAL ANALYSIS OF TREATMENT MODALITIES IN BASAL GANGLIA AND THALAMIC GERMINOMA
Neuro-oncology
Graham R and Abu-Arja M and Stanek J and Bartels U and Cappellano A and Chi S and Cooney T and Dhall G and Finlay J and Fisher M and Friedman G and Gajjar A and Gauvain K and Hoffmann L and AbdelBaki M
12/2020

HGG-35. PEDIATRIC PLEOMORPHIC XANTHOASTROCYTOMA WITH ANAPLASIA TREATED WITH SURGERY AND ADJUVANT CHEMOTHERAPY: A CASE SERIES OF 3 LONG-TERM SURVIVORS
Neuro-oncology
Ronsley R and Dunham C and Yip S and Hukin J and Cheng S
12/2020

RARE-25. RETINAL ASTROCYTOMA mTOR INHIBITOR THERAPY IN TUBEROUS SCLEROSIS MOSAICISM
Neuro-oncology
Evans N and Paton K and Gill H and Hukin J
12/2020

LGG-25. A PHASE 2 STUDY OF TRAMETINIB FOR PATIENTS WITH PEDIATRIC GLIOMA WITH ACTIVATION OF THE MAPK/ERK PATHWAY. TRAM-01
Neuro-oncology
Perreault S and Larouche V and Tabori U and Hawkins C and Lippé S and Ellezam B and Décarie J and Théoret Y and Métras M and Sultan S and Cantin É and Routhier M and Caru M and Legault G and Jabado N
12/2020

NFB-12. TRAMETINIB THERAPY FOR PEDIATRIC PATIENTS WITH REFRACTORY LOW GRADE GLIOMA OR EXTENSIVE SYMPTOMATIC PLEXIFORM NEUROFIBROMA
Neuro-oncology
Hounjet C and Ronsley R and Cheng S and Rassekh S and Duncan W and Dunham C and Gardiner J and Ghag A and P and Ludemann J and Wensley D and Rehmus W and Sargent M and Evans N and Popovska V and Hukin J
12/2020

LGG-19. SPINAL LOW-GRADE GLIOMAS IN CANADIAN CHILDREN: A MULTI-CENTRE RETROSPECTIVE REVIEW
Neuro-oncology
Coltin H and Benipal S and Rassekh S and Nobre L and Bennett J and Tabori U and Wilson B and Mehta V and Beaudoin W and Zelcer S and Cheng S and Hukin J and Hawkins C and Bouffet E and Johnston D
12/2020

Canadian Pediatric Neuro-Oncology Standards of Practice.
Frontiers in oncology
Bennett J and Erker C and Lafay-Cousin L and Ramaswamy V and Hukin J and Vanan MI and Cheng S and Coltin H and Fonseca A and Johnston D and Lo A and Zelcer S and Alvi S and Bowes L and Bartels U
DOI: 10.3389/fonc.2020.593192
PubMed: 33415075
12/2020

Long term toxicity of intracranial germ cell tumor treatment in adolescents and young adults.
Journal of neuro-oncology
Wong J and Goddard K and Laperriere N and Dang J and Bouffet E and Bartels U and Hodgson D and Tyldesley S and Hukin J and Cheng S and Bedard PL and Lo AC
DOI: 10.1007/s11060-020-03642-1
PubMed: 33034840
10/2020

Pontine gliomas a 10-year population-based study: a report from The Canadian Paediatric Brain Tumour Consortium (CPBTC).
Journal of neuro-oncology
Fonseca A and Afzal S and Bowes L and Crooks B and Larouche V and Jabado N and Perreault S and Johnston DL and Zelcer S and Fleming A and Scheinemann K and Silva M and Vanan MI and Bouffet E
DOI: 10.1007/s11060-020-03568-8
PubMed: 32632896
07/2020

Abstracts 10 th Congress WFITN : World Federation of Interventional Therapeutic Neuroradiology - Montreal June 29th - July 3rd 2009
Interventional neuroradiology : journal of peritherapeutic neuroradiology, surgical procedures and related neurosciences
Cekirge S and Hyodo A and Chapot R and Stracke P and El Serwi A and Narata A and Perl I and Fease J and Tubman D and Lylyk P and Lundquist J and Ferrario A and Ceratto R and Scrivano E and Pryor J
07/2020

Cancer and Tumor-Associated Childhood Stroke: Results From the International Pediatric Stroke Study.
Pediatric neurology
Sun LR and Linds A and Sharma M and Rafay M and Vadivelu S and Lee S and Brandão LR and Appavu B and Estepp JH and Hukin J and Hassanein SMA and Chan A and Beslow LA and International Pediatric Stroke Study Group
DOI: 10.1016/j.pediatrneurol.2020.06.002
PubMed: 32951663
06/2020

Locoregional delivery of CAR T cells to the cerebrospinal fluid for treatment of metastatic medulloblastoma and ependymoma.
Nature medicine
Donovan LK and Delaidelli A and Joseph SK and Bielamowicz K and Fousek K and Holgado BL and Manno A and Srikanthan D and Gad AZ and Van Ommeren R and Przelicki D and Richman C and Taylor MD
DOI: 10.1038/s41591-020-0827-2
PubMed: 32341580
04/2020

Pontine Embryonal Tumor With Multilayered Rosettes: An Autopsy Case Exhibiting Extensive Posttreatment Glial and Neuronal Maturation.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society
Levine A and Hukin J and Dunham C
DOI: 10.1177/1093526620912645
PubMed: 32282273
04/2020

Intracranial growing teratoma syndrome (iGTS): an international case series and review of the literature.
Journal of neuro-oncology
Michaiel G and Strother D and Gottardo N and Bartels U and Coltin H and Hukin J and Wilson B and Zelcer S and Hansford JR and Hassall T and AbdelBaki MS and Cole KA and Hoffman L and Lafay-Cousin L
DOI: 10.1007/s11060-020-03486-9
PubMed: 32297094
04/2020

Excellent Outcome of Young Children with Nodular Desmoplastic Medulloblastoma Treated on "Head Start" III: A Multi-Institutional, Prospective Clinical Trial.
Neuro-oncology
Dhall G and O'Neil SH and Ji L and Haley K and Whitaker AM and Nelson MD and Gilles F and Gardner SL and Allen JC and Cornelius AS and Pradhan K and Garvin JH and Olshefski RS and Hukin J and Finlay JL
DOI: 10.1093/neuonc/noaa102
PubMed: 32304218
04/2020

Intracranial Germ Cell Tumors in Adolescents and Young Adults: A 40-Year Multi-Institutional Review of Outcomes
International Journal of Radiation Oncology Biology Physics
Lo, A.C. and Hodgson, D. and Dang, J. and Tyldesley, S. and Bouffet, E. and Bartels, U. and Cheng, S. and Hukin, J. and Bedard, P.L. and Goddard, K. and Laperriere, N.
DOI: 10.1016/j.ijrobp.2019.10.020
2020

A phase 2 study of trametinib for patients with pediatric glioma or plexiform neurofibroma with refractory tumor and activation of the MAPK/ERK pathway: TRAM-01.
BMC cancer
Perreault S and Larouche V and Tabori U and Hawkin C and Lippé S and Ellezam B and Décarie JC and Théoret Y and Métras MÉ and Sultan S and Cantin É and Routhier MÈ and Caru M and Jabado N
DOI: 10.1186/s12885-019-6442-2
PubMed: 31881853
12/2019

Conformal Radiation Therapy for Pediatric Ependymoma, Chemotherapy for Incompletely Resected Ependymoma, and Observation for Completely Resected, Supratentorial Ependymoma
Journal of Clinical Oncology
Thomas E. Merchant and Anne E. Bendel and Noah D. Sabin and Peter C. Burger and Dennis W. Shaw and Eric Chang and Shengjie Wu and Tianni Zhou and David D. Eisenstat and Nicholas K. Foreman and Christine E. Fuller and Edwina Templeton Anderson and Juliette Hukin and Ching C. Lau and Ian F. Pollack and Fred H. Laningham and Robert H. Lustig and Floyd D. Armstrong and Michael H. Handler and Chris Williams-Hughes and Sandra Kessel and Mehmet Kocak and David W. Ellison and Vijay Ramaswamy
DOI: 10.1200/jco.18.01765
04/2019

Canadian patterns of practice for intracranial germ cell tumors in adolescents and young adults.
Journal of neuro-oncology
Lo AC and Laperriere N and Hodgson D and Bouffet E and Nicholson J and McKenzie M and Hukin J and Cheng S and Goddard KJ
DOI: 10.1007/s11060-019-03159-2
PubMed: 30937607
04/2019

Clinical and genetic spectrum of SCN2A-associated episodic ataxia.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
Schwarz N and Bast T and Gaily E and Golla G and Gorman KM and Griffiths LR and Hahn A and Hukin J and King M and Korff C and Miranda MJ and Møller RS and Neubauer B and Smith RA and Smol T and Fazeli W
DOI: 10.1016/j.ejpn.2019.03.001
PubMed: 30928199
03/2019

Conformal radiation therapy for pediatric ependymoma, chemotherapy for incompletely resected ependymoma, and observation for completely resected, supratentorial ependymoma
Journal of Clinical Oncology
Merchant, T.E. and Bendel, A.E. and Sabin, N.D. and Burger, P.C. and Shaw, D.W. and Chang, E. and Wu, S. and Zhou, T. and Eisenstat, D.D. and Foreman, N.K. and Fuller, C.E. and Anderson, E.T. and Hukin, J. and Lau, C.C. and Pollack, I.F. and Laningham, F.H. and Lustig, R.H. and Armstrong, F.D. and Handler, M.H. and Williams-Hughes, C. and Kessel, S. and Kocak, M. and Ellison, D.W. and Ramaswamy, V.
DOI: 10.1200/JCO.18.01765
2019

PDTM-02. STRESS GRANULES ARE INDUCED BY OXIDATIVE STRESS IN PEDIATRIC BRAIN TUMORS AND PREDICT POOR OUTCOME.
Neuro-oncology
Delaidelli A and Luca Negri G and Cho B and Minaker S and El Naggar A and Hukin J and Yip S and Santi M and Maris J and Sorensen P
11/2018

Heterogeneity within the PF-EPN-B ependymoma subgroup
Acta Neuropathologica
DOI: 10.1007/s00401-018-1888-x
08/2018

Canadian Patterns of Practice for Intracranial Germ Cell Tumors in Adolescents and Young Adults
International Journal of Radiation Oncology*Biology*Physics
Andrea Lo and Normand Laperriere and David Hodgson and Eric Bouffet and James Nicholson and Michael McKenzie and Juliette Hukin and Karen Goddard
DOI: 10.1016/j.ijrobp.2018.01.089
07/2018

Narcolepsy and Hypothalamic Region Tumors: Presentation and Evolution
Pediatric Neurology
Alexander G. Weil and Katherine Muir and Juliette Hukin and Alex Desautels and Véronique Martel and Sébastien Perreault
DOI: 10.1016/j.pediatrneurol.2017.12.016
07/2018

IMMU-08. PHASE I TRIAL (NCT02457845) SAFETY, TOLERABILITY AND PRELIMINARY EFFICACY OF IMMUNOVIROTHERAPY WITH HSV G207 IN CHILDREN WITH PROGRESSIVE MALIGNANT SUPRATENTORIAL BRAIN TUMORS
Neuro-Oncology
Gregory Friedman and Asim Bag and Avi Madan-Swain and Rong Li and Kara Kachurak and Diana Osorio and Juliette Hukin and Allison Martin and Devang Pastakia and Matthias Karajannis and Joshua Bernstock and John Fiveash and Alyssa Reddy and Richard Whitley and Yancey Gillespie and James Markert and James Johnston
DOI: 10.1093/neuonc/noy059.324
06/2018

GERM-23. INTRACRANIAL GROWING TERATOMA SYNDROME (IGTS): AN INTERNATIONAL RETROSPECTIVE STUDY.
Neuro-oncology
Michaiel G and Strother D and Gottardo N and Bartels U and Coltin H and Eisenstat DD and Hukin J and Johnston DL and Wilson B and Zelcer S and Hansford JR and Wells O and AbdelBaki MS and Lafay-Cousin L
06/2018

IMMU-08. PHASE I TRIAL (NCT02457845) SAFETY, TOLERABILITY AND PRELIMINARY EFFICACY OF IMMUNOVIROTHERAPY WITH HSV G207 IN CHILDREN WITH PROGRESSIVE MALIGNANT SUPRATENTORIAL BRAIN TUMORS.
Neuro-oncology
Friedman G and Bag A and Madan-Swain A and Li R and Kachurak K and Osorio D and Hukin J and Martin A and Pastakia D and Karajannis M and Bernstock J and Fiveash J and Reddy A and Johnston J
06/2018

GERM-23. INTRACRANIAL GROWING TERATOMA SYNDROME (IGTS): AN INTERNATIONAL RETROSPECTIVE STUDY
Neuro-Oncology
George Michaiel and Douglas Strother and Nicholas Gottardo and Ute Bartels and Hallie Coltin and David D Eisenstat and Juliette Hukin and Donna L Johnston and Beverly Wilson and Shayna Zelcer and Jordan R Hansford and Olivia Wells and Mohamed S AbdelBaki and Mohammad H Abu-Arja and Kristina A Cole and Girish Dhall and Paul G Fisher and Lindsey Hoffman and Sarah E S Leary and Emily E Owens Pickle and Natasha P Smiley and Amy Smith and Anna Vinitsky and Nicholas A Vitanza and Avery Wright and Kee K Yeo and Lionel M L Chow and Maria Kirby and Santosh Valvi and Magimairajan I Vanan and Grace Wong and David Ziegler and Eric Bouffet and Lucie Lafay-Cousin
DOI: 10.1093/neuonc/noy059.270
06/2018

Re-Irradiation in patients with Diffuse Intrinsic Pontine Gliomas: The Canadian Experience
Pediatric Blood & Cancer
DOI: 10.1002/pbc.26988
01/2018

Early changes in white matter predict intellectual outcome in children treated for posterior fossa tumors
NeuroImage: Clinical
Partanen, M. and Bouffet, E. and Laughlin, S. and Strother, D. and Hukin, J. and Skocic, J. and Szulc-Lerch, K. and Mabbott, D.J.
DOI: 10.1016/j.nicl.2018.09.005
2018

A randomized control intervention trial to improve social skills and quality of life in pediatric brain tumor survivors
Psycho-Oncology
Barrera, M. and Atenafu, E.G. and Sung, L. and Bartels, U. and Schulte, F. and Chung, J. and Cataudella, D. and Hancock, K. and Janzen, L. and Saleh, A. and Strother, D. and Downie, A. and Zelcer, S. and Hukin, J. and McConnell, D.
DOI: 10.1002/pon.4385
2018

Immunohistochemical analysis of H3K27me3 demonstrates global reduction in group-A childhood posterior fossa ependymoma and is a powerful predictor of outcome.
Acta neuropathologica
Panwalkar P and Clark J and Ramaswamy V and Hawes D and Yang F and Dunham C and Yip S and Hukin J and Sun Y and Schipper MJ and Chavez L and Margol A and Pekmezci M and Chung C and Banda A and Venneti S
DOI: 10.1007/s00401-017-1752-4
PubMed: 28733933
11/2017

PDTM-49. GLOBAL REDUCTION IN H3K27me3, SIMILAR TO H3K27M MUTANT GLIOMAS, IS A MOLECULAR SURROGATE FOR PEDIATRIC POSTERIOR FOSSA- GROUP A EPENDYMOMAS.
Neuro-oncology
Vennneti S and Panwalkar P and Clark J and Ramaswamy V and Hawes D and Yang F and Dunham C and Yip S and Hukin J and Sun Y and Schipper M and Chavez L and Margol A and Pekmezci M and Chung C and Judkins A
11/2017

RARE-06. CANADIAN PATTERNS OF PRACTICE FOR INTRACRANIAL GERM CELL TUMOURS IN ADOLESCENTS AND YOUNG ADULTS.
Neuro-oncology
Lo A and Laperriere N and Hodgson D and Bouffet E and Nicholson J and McKenzie M and Hukin J and Goddard K
11/2017

RTHP-31. A 40-YEAR MULTI-INSTITUTIONAL REVIEW OF INTRACRANIAL GERM CELL TUMORS IN ADOLESCENTS AND YOUNG ADULT.
Neuro-oncology
Lo A and Goddard K and Hodgson D and Dang J and Tyldesley S and Bouffet E and Bartels U and Cheng S and Hukin J and Bedard P and Tran J and Laperriere N
11/2017

Opsoclonus-Myoclonus Syndrome: A New Era of Improved Prognosis?
Pediatric Neurology
Armine Galstyan and Colin Wilbur and Kathryn Selby and Juliette Hukin
DOI: 10.1016/j.pediatrneurol.2017.03.011
07/2017

Determinants of social competence in pediatric brain tumor survivors who participated in an intervention study
Supportive Care in Cancer
Maru Barrera and Eshetu G. Atenafu and Fiona Schulte and Ute Bartels and Lillian Sung and Laura Janzen and Joanna Chung and Danielle Cataudella and Kelly Hancock and Amani Saleh and Douglas Strother and Dina McConnell and Andrea Downie and Juliette Hukin and Shayna Zelcer
DOI: 10.1007/s00520-017-3708-6
04/2017

Determinants of quality of life outcomes for survivors of pediatric brain tumors
Pediatric Blood & Cancer
Maru Barrera and Eshetu G. Atenafu and Fiona Schulte and Ute Bartels and Lillian Sung and Laura Janzen and Joanna Chung and Danielle Cataudella and Kelly Hancock and Amani Saleh and Douglas Strother and Dina McConnell and Andrea Downie and Juliette Hukin and Shayna Zelcer
DOI: 10.1002/pbc.26481
03/2017

Atypical teratoid rhabdoid tumor in the first year of life: the Canadian ATRT registry experience and review of the literature.
Journal of neuro-oncology
Fossey M and Li H and Afzal S and Carret AS and Eisenstat DD and Fleming A and Hukin J and Hawkins C and Jabado N and Johnston D and Brown T and Larouche V and Scheinemann K and Lafay-Cousin L
DOI: 10.1007/s11060-016-2353-0
PubMed: 28102486
03/2017

Longitudinal Outcomes in the 2014 Acute Flaccid Paralysis Cluster in Canada
Journal of Child Neurology
Yea, C. and Bitnun, A. and Robinson, J. and Mineyko, A. and Barton, M. and Mah, J.K. and Vajsar, J. and Richardson, S. and Licht, C. and Brophy, J. and Crone, M. and Desai, S. and Hukin, J. and Jones, K. and Muir, K. and Pernica, J.M. and Pless, R. and Pohl, D. and Rafay, M.F. and Selby, K. and Venkateswaran, S. and Bernard, G. and Yeh, E.A.
DOI: 10.1177/0883073816680770
2017

Integrated (epi)-Genomic Analyses Identify Subgroup-Specific Therapeutic Targets in CNS Rhabdoid Tumors.
Cancer cell
Torchia J and Golbourn B and Feng S and Ho KC and Sin-Chan P and Vasiljevic A and Norman JD and Guilhamon P and Garzia L and Agamez NR and Lu M and Chan TS and Picard D and Huang A
DOI: 10.1016/j.ccell.2016.11.003
PubMed: 27960086
12/2016

Phase II Weekly Vinblastine for Chemotherapy-Naïve Children With Progressive Low-Grade Glioma: A Canadian Pediatric Brain Tumor Consortium Study
Journal of Clinical Oncology
Alvaro Lassaletta and Katrin Scheinemann and Shayna M. Zelcer and Juliette Hukin and Beverley A. Wilson and Nada Jabado and Anne Sophie Carret and Lucie Lafay-Cousin and Valerie Larouche and Cynthia E. Hawkins and Gregory Russell Pond and Ken Poskitt and Daniel Keene and Donna L. Johnston and David D. Eisenstat and Rahul Krishnatry and Matthew Mistry and Anthony Arnoldo and Vijay Ramaswamy and Annie Huang and Ute Bartels and Uri Tabori and Eric Bouffet
DOI: 10.1200/jco.2016.68.1585
10/2016

Episodic ataxia associated with a de novo SCN2A mutation
European Journal of Paediatric Neurology
Emma L. Leach and Clara D.M. van Karnebeek and Katelin N. Townsend and Maja Tarailo-Graovac and Juliette Hukin and William T. Gibson
DOI: 10.1016/j.ejpn.2016.05.020
09/2016

Targeted detection of genetic alterations reveal the prognostic impact of H3K27M and MAPK pathway aberrations in paediatric thalamic glioma
Acta Neuropathologica Communications
Scott Ryall and Rahul Krishnatry and Anthony Arnoldo and Pawel Buczkowicz and Matthew Mistry and Robert Siddaway and Cino Ling and Sanja Pajovic and Man Yu and Joshua B. Rubin and Juliette Hukin and Paul Steinbok and Ute Bartels and Eric Bouffet and Uri Tabori and Cynthia Hawkins
DOI: 10.1186/s40478-016-0353-0
08/2016

Therapeutic Impact of Cytoreductive Surgery and Irradiation of Posterior Fossa Ependymoma in the Molecular Era: A Retrospective Multicohort Analysis.
Journal of clinical oncology : official journal of the American Society of Clinical Oncology
Ramaswamy V and Hielscher T and Mack SC and Lassaletta A and Lin T and Pajtler KW and Jones DT and Luu B and Cavalli FM and Aldape K and Remke M and Mynarek M and Rutkowski S and Taylor MD
DOI: 10.1200/jco.2015.65.7825
PubMed: 27269943
07/2016

White matter and information processing speed following treatment with cranial-spinal radiation for pediatric brain tumor.
Neuropsychology
Nadia Scantlebury and Eric Bouffet and Suzanne Laughlin and Douglas Strother and Dina McConnell and Juliette Hukin and Christopher Fryer and Normand Laperriere and Isabelle Montour-Proulx and Daniel Keene and Adam Fleming and Nada Jabado and Fang Liu and Lily Riggs and Nicole Law and Donald J. Mabbott
DOI: 10.1037/neu0000258
05/2016

Ophthalmological outcomes of patients treated for pineal region tumors
Journal of Neurosurgery: Pediatrics
Elizabeth V. Hankinson and Christopher J. Lyons and Juliette Hukin and David D. Cochrane
DOI: 10.3171/2015.10.peds15415
05/2016

Eye Findings on Vigabatrin and Taurine Treatment in Two Patients with Succinic Semialdehyde Dehydrogenase Deficiency
Neuropediatrics
Juliette Hukin and Sylvia Stockler-Ipsiroglu and Maryam Aroichane and Gabriella-Ana Horvath
DOI: 10.1055/s-0036-1583183
04/2016

Phase II weekly vinblastine for chemotherapy-naïve children with progressive low-grade glioma: A Canadian pediatric brain tumor consortium study
Journal of Clinical Oncology
Lassaletta, A. and Scheinemann, K. and Zelcer, S.M. and Hukin, J. and Wilson, B.A. and Jabado, N. and Carret, A.S. and Lafay-Cousin, L. and Larouche, V. and Hawkins, C.E. and Pond, G.R. and Poskitt, K. and Keene, D. and Johnston, D.L. and Eisenstat, D.D. and Krishnatry, R. and Mistry, M. and Arnoldo, A. and Ramaswamy, V. and Huang, A. and Bartels, U. and Tabori, U. and Bouffet, E.
DOI: 10.1200/JCO.2016.68.1585
2016

Ophthalmological outcomes of patients treated for pineal region tumors
Journal of Neurosurgery: Pediatrics
Hankinson, E.V. and Lyons, C.J. and Hukin, J. and Cochrane, D.D.
DOI: 10.3171/2015.10.PEDS15415
2016

Therapeutic impact of cytoreductive surgery and irradiation of posterior fossa ependymoma in the molecular era: A retrospective multicohort analysis
Journal of Clinical Oncology
Ramaswamy, V. and Hielscher, T. and Mack, S.C. and Lassaletta, A. and Lin, T. and Pajtler, K.W. and Jones, D.T.W. and Luu, B. and Cavalli, F.M.G. and Aldape, K. and Remke, M. and Mynarek, M. and Rutkowski, S. and Gururangan, S. and McLendon, R.E. and Lipp, E.S. and Dunham, C. and Hukin, J. and Eisenstat, D.D. and Fulton, D. and Van Landeghem, F.K.H. and Santi, M. and Van Veelen, M.-L.C. and Van Meir, E.G. and Osuka, S. and Fan, X. and Muraszko, K.M. and Tirapelli, D.P.C. and Oba-Shinjo, S.M. and Marie, S.K.N. and Carlotti, C.G. and Lee, J.Y. and Rao, A.A.N. and Giannini, C. and Faria, C.C. and Nunes, S. and Mora, J. and Hamilton, R.L. and Hauser, P. and Jabado, N. and Petrecca, K. and Jung, S. and Massimi, L. and Zollo, M. and Cinalli, G. and Bognár, L. and Klekner, A. and Hortobágyi, T. and Leary, S. and Ermoian, R.P. and Olson, J.M. and Leonard, J.R. and Gardner, C. and Grajkowska, W.A. and Chambless, L.B. and Cain, J. and Eberhart, C.G. and Ahsan, S. and Massimino, M. and Giangaspero, F. and Buttarelli, F.R. and Packer, R.J. and Emery, L. and Yong, W.H. and Soto, H. and Liau, L.M. and Everson, R. and Grossbach, A. and Shalaby, T. and Grotzer, M. and Karajannis, M.A. and Zagzag, D. and Wheeler, H. and Von Hoff, K. and Alonso, M.M. and Tuñon, T. and Schüller, U. and Zitterbart, K. and Sterba, J. and Chan, J.A. and Guzman, M. and Elbabaa, S.K. and Colman, H. and Dhall, G. and Fisher, P.G. and Fouladi, M. and Gajjar, A. and Goldman, S. and Hwang, E. and Kool, M. and Ladha, H. and Vera-Bolanos, E. and Wani, K. and Lieberman, F. and Mikkelsen, T. and Omuro, A.M. and Pollack, I.F. and Prados, M. and Robins, H.I. and Soffietti, R. and Wu, J. and Metellus, P. and Tabori, U. and Bartels, U. and Bouffet, E. and Hawkins, C.E. and Rutka, J.T. and Dirks, P. and Pfister, S.M. and Merchant, T.E. and Gilbert, M.R. and Armstrong, T.S. and Korshunov, A. and Ellison, D.W. and Taylor, M.D.
DOI: 10.1200/JCO.2015.65.7825
2016

Pediatric thalamic tumors in the MRI era: a Canadian perspective
Child's Nervous System
Steinbok, P. and Gopalakrishnan, C.V. and Hengel, A.R. and Vitali, A.M. and Poskitt, K. and Hawkins, C. and Drake, J. and Lamberti-Pasculli, M. and Ajani, O. and Hader, W. and Mehta, V. and McNeely, P.D. and McDonald, P.J. and Ranger, A. and Vassilyadi, M. and Atkinson, J. and Ryall, S. and Eisenstat, D.D. and Hukin, J.
DOI: 10.1007/s00381-015-2968-z
2016

Assessing the accuracy of death records and pre-mortem clinical diagnoses in children diagnosed with brain tumors: A retrospective chart review of children in British Columbia, Canada
Pathology - Research and Practice
Haroon Hasan and Glenda Hendson and A. Fuchsia Howard and Juliette Hukin and Christopher Dunham and Tareq Ahmed and Andrea C. Lo and Karen Goddard
DOI: 10.1016/j.prp.2015.06.008
10/2015

Intracystic interferon-a treatment leads to neurotoxicity in craniopharyngioma: case report
Journal of Neurosurgery: Pediatrics
Julia Sharma and Christopher M. Bonfield and Ash Singhal and Juliette Hukin and Paul Steinbok
DOI: 10.3171/2015.2.peds14656
09/2015

Molecular subgroups of atypical teratoid rhabdoid tumours in children: an integrated genomic and clinicopathological analysis.
The Lancet. Oncology
Torchia J and Picard D and Lafay-Cousin L and Hawkins CE and Kim SK and Letourneau L and Ra YS and Ho KC and Chan TS and Sin-Chan P and Dunham CP and Yip S and Ng HK and Lu JQ and Albrecht S and Huang A
DOI: 10.1016/s1470-2045(15)70114-2
PubMed: 25882982
05/2015

AT-07 * SUCCESSFUL TREATMENT OF ATRT PATIENTS WITHOUT ADJUVANT RADIATION: A MULTI INSTITUTIONAL CANADIAN EXPERIENCE
Neuro-Oncology
D. Ku and L. Lafay-Cousin and C. Fryer and J. Hukin and D. Strother and A. Huang and E. Bouffet
DOI: 10.1093/neuonc/nov061.6
04/2015

Neurocognitive evaluation of long term survivors of atypical teratoid rhabdoid tumors (ATRT): The Canadian registry experience
Pediatric Blood & Cancer
Lucie Lafay-Cousin and Taryn Fay-McClymont and Donna Johnston and Chris Fryer and Katrin Scheinemann and Adam Fleming and Juliette Hukin and Laura Janzen and Sharon Guger and Douglas Strother and Donald Mabbott and Annie Huang and Eric Bouffet
DOI: 10.1002/pbc.25441
03/2015

EZH2 expression is a prognostic factor in childhood intracranial ependymoma: A Canadian Pediatric Brain Tumor Consortium study
Cancer
Amanda M. Li and Christopher Dunham and Uri Tabori and Anne-Sophie Carret and P. Daniel McNeely and Donna Johnston and Lucie Lafay-Cousin and Beverly Wilson and David D. Eisenstat and Nada Jabado and Shayna Zelcer and Mariana Silva and Katrin Scheinemann and Christopher Fryer and Glenda Hendson and Abbas Fotovati and Cynthia Hawkins and Stephen Yip and Sandra E. Dunn and Juliette Hukin
DOI: 10.1002/cncr.29198
01/2015

Molecular subgroups of atypical teratoid rhabdoid tumours in children: An integrated genomic and clinicopathological analysis
The Lancet Oncology
Torchia, J. and Picard, D. and Lafay-Cousin, L. and Hawkins, C.E. and Kim, S.-K. and Letourneau, L. and Ra, Y.-S. and Ho, K.C. and Chan, T.S.Y. and Sin-Chan, P. and Dunham, C.P. and Yip, S. and Ng, H.-K. and Lu, J.-Q. and Albrecht, S. and Pimentel, J. and Chan, J.A. and Somers, G.R. and Zielenska, M. and Faria, C.C. and Roque, L. and Baskin, B. and Birks, D. and Foreman, N. and Strother, D. and Klekner, A. and Garami, M. and Hauser, P. and Hortobágyi, T. and Bognár, L. and Wilson, B. and Hukin, J. and Carret, A.-S. and Van Meter, T.E. and Nakamura, H. and Toledano, H. and Fried, I. and Fults, D. and Wataya, T. and Fryer, C. and Eisenstat, D.D. and Scheineman, K. and Johnston, D. and Michaud, J. and Zelcer, S. and Hammond, R. and Ramsay, D.A. and Fleming, A.J. and Lulla, R.R. and Fangusaro, J.R. and Sirachainan, N. and Larbcharoensub, N. and Hongeng, S. and Barakzai, M.A. and Montpetit, A. and Stephens, D. and Grundy, R.G. and Schüller, U. and Nicolaides, T. and Tihan, T. and Phillips, J. and Taylor, M.D. and Rutka, J.T. and Dirks, P. and Bader, G.D. and Warmuth-Metz, M. and Rutkowski, S. and Pietsch, T. and Judkins, A.R. and Jabado, N. and Bouffet, E. and Huang, A.
DOI: 10.1016/S1470-2045(15)70114-2
2015

Ependymoma
Pediatric Neuro-oncology
Juliette Hukin and John-Paul Kilday and Uri Tabori
DOI: 10.1007/978-1-4939-1541-5
2015

Low Grade Glioma
Pediatric Neuro-oncology
Katrin Scheinemann and Juliette Hukin
DOI: 10.1007/978-1-4939-1541-5_9
2015

Ependymoma
Pediatric Neuro-oncology
Juliette Hukin and John-Paul Kilday and Uri Tabori
DOI: 10.1007/978-1-4939-1541-5_13
2015

Intracystic interferon-a treatment leads to neurotoxicity in craniopharyngioma: Case report
Journal of Neurosurgery: Pediatrics
Sharma, J. and Bonfield, C.M. and Singhal, A. and Hukin, J. and Steinbok, P.
DOI: 10.3171/2015.2.PEDS14656
2015

The role of resection alone in select children with intracranial ependymoma: the Canadian Pediatric Brain Tumour Consortium experience
Child's Nervous System
Ailon, T. and Dunham, C. and Carret, A.-S. and Tabori, U. and Mcneely, P.D. and Zelcer, S. and Wilson, B. and Lafay-Cousin, L. and Johnston, D. and Eisenstat, D.D. and Silva, M. and Jabado, N. and Goddard, K.J. and Fryer, C. and Hendson, G. and Hawkins, C. and Dunn, S. and Yip, S. and Singhal, A. and Hukin, J.
DOI: 10.1007/s00381-014-2575-4
2015

White matter compromise predicts poor intellectual outcome in survivors of pediatric low-grade glioma
Neuro-Oncology
F. Liu and N. Scantlebury and U. Tabori and E. Bouffet and S. Laughlin and D. Strother and D. McConnell and J. Hukin and C. Fryer and M.-E. Briere and I. Montour-Proulx and D. Keene and F. Wang and D. J. Mabbott
DOI: 10.1093/neuonc/nou306
11/2014

Epidemiology of malignant pontine gliomas (MPG) in the paediatric population in Canada: A study of the Canadian paediatric brain tumour consortium (CPBTC)
Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques
Samina Afzal and Anne-Sophie Carret and Adam Fleming and Valerie Larouche and Shayna Zelcer and Donna L. Johnston and Maria Kostova and Chris Mpofu and Douglas Strother and Lucie Lafay-Cousin and David Eisenstat and Chris Fryer and Juliette Hukin and Ute Bartels and Eric Bouffet
DOI: 10.1017/cjn.2014.86
10/2014

Pleomorphic xanthoastrocytoma of the spinal cord: case report and literature review
Clinical Neuropathology
Sumit Das and Stephen Yip and Juliette Hukin and Douglas Cochrane and Christopher Dunham
DOI: 10.5414/np300689
05/2014

Genomic analysis of diffuse intrinsic pontine gliomas identifies three molecular subgroups and recurrent activating ACVR1 mutations.
Nature genetics
Buczkowicz P and Hoeman C and Rakopoulos P and Pajovic S and Letourneau L and Dzamba M and Morrison A and Lewis P and Bouffet E and Bartels U and Zuccaro J and Agnihotri S and Ryall S and Hawkins C
DOI: 10.1038/ng.2936
PubMed: 24705254
05/2014

Late effects in survivors of childhood CNS tumors treated on Head Start I and II protocols
Pediatric Blood & Cancer
Aniket Saha and Christina G. Salley and Preeti Saigal and Linda Rolnitzky and Judith Goldberg and Suzanne Scott and Randal Olshefski and Juliette Hukin and Stephen A. Sands and Jonathan Finlay and Sharon L. Gardner
DOI: 10.1002/pbc.25064
05/2014

Multimodality therapy for CNS mixed malignant germ cell tumors (MMGCT): results of a phase II multi-institutional study
Journal of Neuro-Oncology
Patricia L. Robertson and Regina Jakacki and Juliette Hukin and Joao Siffert and Jeffrey C. Allen
DOI: 10.1007/s11060-013-1306-0
04/2014

De-escalation of therapy for pediatric medulloblastoma: Trade-offs between quality of life and survival
Pediatric Blood & Cancer
Natalie Henrich and Carlo A. Marra and Louise Gastonguay and Donald Mabbott and David Malkin and Chris Fryer and Eric Bouffet and Michael D. Taylor and Juliette Hukin and Nadia Scantlebury and Larry Lynd
DOI: 10.1002/pbc.24990
02/2014

Changes to Memory Structures in Children Treated for Posterior Fossa Tumors
Journal of the International Neuropsychological Society
Lily Riggs and Eric Bouffet and Suzanne Laughlin and Normand Laperriere and Fang Liu and Jovanka Skocic and Nadia Scantlebury and Frank Wang and Nicholas J. Schoenhoff and Douglas Strother and Juliette Hukin and Christopher Fryer and Dina McConnell and Donald J. Mabbott
DOI: 10.1017/s135561771300129x
01/2014

Chemotherapy for Tumors
Nervous System of Children
2014

Changes to memory structures in children treated for posterior fossa tumors
Journal of the International Neuropsychological Society
Riggs, L. and Bouffet, E. and Laughlin, S. and Laperriere, N. and Liu, F. and Skocic, J. and Scantlebury, N. and Wang, F. and Schoenhoff, N.J. and Strother, D. and Hukin, J. and Fryer, C. and McConnell, D. and Mabbott, D.J.
DOI: 10.1017/S135561771300129X
2014

Growing teratoma syndrome in intracranial non-germinomatous germ cell tumors (iNGGCTs): A risk for secondary malignant transformation - A report of two cases
Child's Nervous System
Glass, T. and Cochrane, D.D. and Rassekh, S.R. and Goddard, K. and Hukin, J.
DOI: 10.1007/s00381-013-2295-1
2014

Pleomorphic xanthoastrocytoma of the spinal cord: Case report and literature review
Clinical Neuropathology
Das, S. and Yip, S. and Hukin, J. and Cochrane, D. and Dunham, C.
DOI: 10.5414/NP300689
2014

Optic pathway gliomas in adolescence--time to challenge treatment choices?
Neuro-Oncology
A. Lee Chong and J. D. Pole and K. Scheinemann and J. Hukin and U. Tabori and A. Huang and E. Bouffet and U. Bartels
DOI: 10.1093/neuonc/nos312
01/2013

Novel mutations in FA2H-associated neurodegeneration: An underrecognized condition?
Journal of Child Neurology
Rupps, R. and Hukin, J. and Balicki, M. and Mercimek-Mahmutoglu, S. and Rolfs, A. and Dias, C.
DOI: 10.1177/0883073812458538
2013

Personalizing the treatment of pediatric medulloblastoma: Polo-like kinase 1 as a molecular target in high-risk children
Cancer Research
Triscott, J. and Lee, C. and Foster, C. and Manoranjan, B. and Pambid, M.R. and Berns, R. and Fotovati, A. and Venugopal, C. and O'Halloran, K. and Narendran, A. and Hawkins, C. and Ramaswamy, V. and Bouffet, E. and Taylor, M.D. and Singhal, A. and Hukin, J. and Rassekh, R. and Yip, S. and Northcott, P. and Singh, S.K. and Dunham, C. and Dunn, S.E.
DOI: 10.1158/0008-5472.CAN-12-4331
2013

Clinical and neuroanatomical predictors of cerebellar mutism syndrome
Neuro-Oncology
N. Law and M. Greenberg and E. Bouffet and M. D. Taylor and S. Laughlin and D. Strother and C. Fryer and D. McConnell and J. Hukin and C. Kaise and F. Wang and D. J. Mabbott
DOI: 10.1093/neuonc/nos160
09/2012

Phase II Study of Weekly Vinblastine in Recurrent or Refractory Pediatric Low-Grade Glioma
Journal of Clinical Oncology
Eric Bouffet and Regina Jakacki and Stewart Goldman and Darren Hargrave and Cynthia Hawkins and Manohar Shroff and Juliette Hukin and Ute Bartels and Nicholas Foreman and Stewart Kellie and Joanne Hilden and Michael Etzl and Beverly Wilson and Derek Stephens and Uri Tabori and Sylvain Baruchel
DOI: 10.1200/jco.2011.34.5843
04/2012

Intracranial tumors in infants: long-term functional outcome, survival, and its predictors
Child's Nervous System
Shibu Pillai and Mary Metrie and Christopher Dunham and Michael Sargent and Juliette Hukin and Paul Steinbok
DOI: 10.1007/s00381-012-1707-y
02/2012

Atypical Teratoid Rhabdoid Tumors (ATRTs): The British Columbia's Children's Hospital's Experience, 1986-2006
Brain Pathology
Adam J. Fleming and Juliette Hukin and Rod Rassekh and Christopher Fryer and James Kim and Anat Stemmer-Rachamimov and Diane K. Birks and Annie Huang and Stephen Yip and Christopher Dunham
DOI: 10.1111/j.1750-3639.2011.00561.x
02/2012

Cystic Craniopharyngiomas: Intratumoral Bleomycin Therapy
Tumors of the Central Nervous System, Volume 8
Paul Steinbok and Juliette Hukin
DOI: 10.1007/978-94-007-4213-0_23
2012

Supratentorial primitive neuroectodermal tumors
Tumors of the Central Nervous System, Volume 4: Brain Tumors (Part 2)
Singh, M. and Hukin, J.
DOI: 10.1007/978-94-007-1706-0_2
2012

Phase II study of weekly vinblastine in recurrent or refractory pediatric low-grade glioma
Journal of Clinical Oncology
Bouffet, E. and Jakacki, R. and Goldman, S. and Hargrave, D. and Hawkins, C. and Shroff, M. and Hukin, J. and Bartels, U. and Foreman, N. and Kellie, S. and Hilden, J. and Etzl, M. and Wilson, B. and Stephens, D. and Tabori, U. and Baruchel, S.
DOI: 10.1200/JCO.2011.34.5843
2012

Cerebello–thalamo–cerebral connections in pediatric brain tumor patients: Impact on working memory
NeuroImage
Nicole Law and Eric Bouffet and Suzanne Laughlin and Normand Laperriere and Marie-Eve Brière and Douglas Strother and Dina McConnell and Juliette Hukin and Christopher Fryer and Conrad Rockel and Jolynn Dickson and Donald Mabbott
DOI: 10.1016/j.neuroimage.2011.03.065
06/2011

The use and effectiveness of temozolomide in children with central nervous system tumours: a survey from the Canadian Paediatric Brain Tumour Consortium
Current Oncology
U. Bartels and S. Baruchel and A.S. Carret and B. Crooks and J. Hukin and D. Johnston and M. Silva and D. Strother and B. Wilson and S. Zelcer and D. Eisenstat and L. Sung and E. Bouffet
DOI: 10.3747/co.v18i1.675
02/2011

Childhood CNS Pediatric Primitive Neuroectodermal Tumors
Tumors of the Central Nervous System
11/2010

Intracystic treatments for craniopharyngioma
Neurosurgical Focus
Paul Steinbok and Juliette Hukin
DOI: 10.3171/2010.1.focus09315
04/2010

Late mortality in pediatric patients with craniopharyngioma
Journal of Neuro-Oncology
Johannes Visser and Juliette Hukin and Michael Sargent and Paul Steinbok and Karen Goddard and Chris Fryer
DOI: 10.1007/s11060-010-0145-5
03/2010

Intracystic treatments for craniopharyngioma
Neurosurgical Focus
Steinbok, P. and Hukin, J.
DOI: 10.3171/2010.1.FOCUS09315
2010

A multi-centre Canadian pilot study of metronomic temozolomide combined with radiotherapy for newly diagnosed paediatric brainstem glioma
European Journal of Cancer
Julia R. Sharp and Eric Bouffet and Diana Stempak and Janet Gammon and Derek Stephens and Donna L. Johnston and David Eisenstat and Juliette Hukin and Yvan Samson and Ute Bartels and Uri Tabori and Annie Huang and Sylvain Baruchel
DOI: 10.1016/j.ejca.2010.06.115
2010

A Canadian paediatric brain tumour consortium (CPBTC) phase II molecularly targeted study of imatinib in recurrent and refractory paediatric central nervous system tumours
European Journal of Cancer
Sylvain Baruchel and Julia R. Sharp and Ute Bartels and Juliette Hukin and Isaac Odame and Carol Portwine and Doug Strother and Chris Fryer and Jackie Halton and Merrill J. Egorin and Rui Manuel Reis and Olga Martinho and Diana Stempak and Cynthia Hawkins and Janet Gammon and Eric Bouffet
DOI: 10.1016/j.ejca.2009.05.008
09/2009

Occurrence of Basal Ganglia Germ Cell Tumors Without a Mass
Archives of Neurology
Salah Almubarak and Yee-Chiung Gan and Paul Steinbok and Glenda Hendson and Ken Poskitt and Helen Nadel and Karen Goddard and Juliette Hukin
DOI: 10.1001/archneurol.2009.74
06/2009

Atypical Presentation of Basal Ganglia Germ Cell Tumors in Children
Journal of Neurosurgery: Pediatrics
Paul Steinbok and Salah Almubarak and Peter Gan and Glenda Hendson and Kenneth Poskitt and Helen Nadel and Karen Goddard and Juliette Hukin
DOI: 10.3171/ped/2008/1/4/paper11
04/2008

Intensive chemotherapy followed by consolidative myeloablative chemotherapy with autologous hematopoietic cell rescue (AuHCR) in young children with newly diagnosed supratentorial primitive neuroectodermal tumors (sPNETs): Report of the Head Start I and II experience
Pediatric Blood & Cancer
Jason Fangusaro and Jonathan Finlay and Richard Sposto and Lingyun Ji and Monirath Saly and Stergios Zacharoulis and Shahab Asgharzadeh and Minnie Abromowitch and Randal Olshefski and Steven Halpern and Ronald Dubowy and Melanie Comito and Blanca Diez and Stewart Kellie and Juliette Hukin and Marc Rosenblum and Ira Dunkel and Douglas C. Miller and Jeffrey Allen and Sharon Gardner
DOI: 10.1002/pbc.21307
02/2008

Carboplatin hypersensitivity reaction in pediatric patients with low-grade glioma
Cancer
Lucie Lafay-Cousin and Lillian Sung and Anne-Sophie Carret and Juliette Hukin and Beverly Wilson and Donna L. Johnston and Shayna Zelcer and Mariana Silva and Isaac Odame and Chris Mpofu and Douglas Strother and Eric Bouffet
DOI: 10.1002/cncr.23249
2008

Concurrent carbogen and radiation therapy in children with high-risk brainstem gliomas
Pediatric Blood and Cancer
Aquino-Parsons, C. and Hukin, J. and Green, A.
DOI: 10.1002/pbc.21057
2008

Isolated sulfite oxidase deficiency in the newborn: lactic acidaemia and leukoencephalopathy.
Neuropediatrics
Basheer SN and Waters PJ and Lam CW and Acquaviva-Bourdain C and Hendson G and Poskitt K and Hukin J
DOI: 10.1055/s-2007-981484
PubMed: 17607604
02/2007

Outcome for young children newly diagnosed with ependymoma, treated with intensive induction chemotherapy followed by myeloablative chemotherapy and autologous stem cell rescue
Pediatric Blood and Cancer
Zacharoulis, S. and Levy, A. and Chi, S.N. and Gardner, S. and Rosenblum, M. and Miller, D.C. and Dunkel, I. and Diez, B. and Sposto, R. and Ji, L. and Asgharzadeh, S. and Hukin, J. and Belasco, J. and Dubowy, R. and Kellie, S. and Termuhlen, A. and Finlay, J.
DOI: 10.1002/pbc.20935
2007

Intracystic bleomycin therapy for craniopharyngioma in children
Cancer
Juliette Hukin and Paul Steinbok and Lucie Lafay-Cousin and Glenda Hendson and Douglas Strother and Claude Mercier and Yvan Samson and William Howes and Eric Bouffet
DOI: 10.1002/cncr.22633
2007

Outcome of secondary high-grade glioma in children previously treated for a malignant condition: A study of the Canadian Pediatric Brain Tumour Consortium
Radiotherapy and Oncology
Anne-Sophie Carret and Uri Tabori and Bruce Crooks and Juliette Hukin and Isaac Odame and Donna L. Johnston and Daniel L. Keene and Carolyn Freeman and Eric Bouffet
DOI: 10.1016/j.radonc.2006.08.005
10/2006

Distinctive clinical course and pattern of relapse in adolescents with medulloblastoma
International Journal of Radiation Oncology*Biology*Physics
Uri Tabori and Lillian Sung and Juliette Hukin and Normand Laperriere and Bruce Crooks and Anne-Sophie Carret and Mariana Silva and Isaac Odame and Chris Mpofu and Douglas Strother and Beverly Wilson and Yvan Samson and Eric Bouffet
DOI: 10.1016/j.ijrobp.2005.07.962
02/2006

The causes and timing of death of craniopharyngiomas patients diagnosed before the age of 17 years
Pediatric Blood & Cancer
10/2005

Asynchronous burst-suppression in a child with callosal Ki-1 anaplastic large cell lymphoma.
Neurology
Hukin J and Davey A and Wong P and Hendson G and Aquino-Parsons C and Wu J and Sargent M
DOI: 10.1212/01.wnl.0000176070.34107.f6
PubMed: 16186544
09/2005

Childhood craniopharyngioma: Vancouver experience
Child's Nervous System
Juliette Hukin and Johann Visser and Michael Sargent and Karen Goddard and Chris Fryer and Paul Steinbok
DOI: 10.1007/s00381-005-1220-7
06/2005

Medulloblastoma in the second decade of life: A specific group with respect to toxicity and management
Cancer
Uri Tabori and Lillian Sung and Juliette Hukin and Normand Laperriere and Bruce Crooks and Anne-Sophie Carret and Mariana Silva and Isaac Odame and Chris Mpofu and Douglas Strother and Beverly Wilson and Yvan Samson and Eric Bouffet and Canadian Pediatric Brain Tumor Consortium
DOI: 10.1002/cncr.21003
2005

Malaysian Siblings with Friedreich Ataxia and Chorea: A Novel Deletion in the Frataxin Gene
The Canadian Journal of Neurological Sciences
Siân D. Spacey and Blazej I. Szczygielski and Sean P. Young and Juliette Hukin and Kathy Selby and Terrance P. Snutch
DOI: 10.1017/s0317167100003498
08/2004

Malaysian siblings with Friedreich ataxia and chorea: A novel deletion in the frataxin gene
Canadian Journal of Neurological Sciences
Spacey, S.D. and Szczygielski, B.I. and Young, S.P. and Hukin, J. and Selby, K. and Snutch, T.P.
DOI: 10.1017/S0317167100003498
2004

Leptomeningeal dissemination at diagnosis of pediatric low-gradeneuroepithelial tumors
Neuro-Oncology
Juliette Hukin and Joao Siffert and Henry Cohen and Linda Velasquez and David Zagzag and Jeffrey Allen
DOI: 10.1215/s1152851702000297
07/2003

Leptomeningeal dissemination at diagnosis of pediatric low-grade neuroepithelial tumors
Neuro-Oncology
Hukin, J. and Siffert, J. and Cohen, H. and Velasquez, L. and Zagzag, D. and Allen, J.
DOI: 10.1215/S1152851702000297
2003

Leptomeningeal dissemination in children with progressive low-grade neuroepithelial tumors
Neuro-Oncology
Juliette Hukin and Joao Siffert and Linda Velasquez and David Zagzag and Jeffrey Allen
DOI: 10.1215/s1522851701000680
10/2002

Tenascin-C promotes microvascular cell migration and phosphorylation of focal adhesion kinase.
Cancer research
Zagzag D and Shiff B and Jallo GI and Greco MA and Blanco C and Cohen H and Hukin J and Allen JC and Friedlander DR
PubMed: 11980665
05/2002

Tenascin-C promotes microvascular cell migration and phosphorylation of focal adhesion kinase
Cancer Research
Zagzag, D. and Shiff, B. and Jallo, G.I. and Alba Greco, M. and Blanco, C. and Cohen, H. and Hukin, J. and Allen, J.C. and Friedlander, D.R.
2002

Leptomeningeal dissemination in children with progressive low-grade neuroepithelial tumors
Neuro-Oncology
Hukin, J. and Siffert, J. and Velasquez, L. and Zagzag, D. and Allen, J.
DOI: 10.1215/15228517-4-4-253
2002

Hyperbaric oxygen therapy for cerebral palsy: two complications of treatment.
Pediatrics
Nuthall G and Seear M and Lepawsky M and Wensley D and Skippen P and Hukin J
DOI: 10.1542/peds.106.6.e80
PubMed: 11099623
12/2000

Intratumoral Therapy with Bleomycin for Cystic Craniopharyngiomas in Children
Pediatric Neurosurgery
Walter J. Hader and Paul Steinbok and Juliette Hukin and Chris Fryer
DOI: 10.1159/000055955
2000

Brain Tumours
Primary Pediatric Care, 4th Edition
03/1999

Encephalopathy complicating Henoch-Schönlein purpura: reversible MRI changes.
Pediatric neurology
Woolfenden AR and Hukin J and Poskitt KJ and Connolly MB
DOI: 10.1016/s0887-8994(98)00027-7
PubMed: 9682892
07/1998

Case-control study of primary human herpesvirus 6 infection in children with febrile seizures.
Pediatrics
Hukin J and Farrell K and MacWilliam LM and Colbourne M and Waida E and Tan R and Mroz L and Thomas E
DOI: 10.1542/peds.101.2.e3
PubMed: 9445513
02/1998

Clinical manifestations of childhood ependymoma: A multitude of syndromes
Pediatric Neurosurgery
Allen, J.C. and Siffert, J. and Hukin, J.
DOI: 10.1159/000028619
1998

Treatment of Intracranial Ependymoma by Surgery Alone
Pediatric Neurosurgery
Juliette Hukin and Fred Epstein and Dan Lefton and Jeffrey Allen
DOI: 10.1159/000028683
1998

Encephalopathy complicating henoch schonlein purpura: Reversible MRI changes
Pediatric Neurology
Woolfenden, A.R. and Hukin, J. and Poskitt, K.J. and Connolly, M.B.
DOI: 10.1016/S0887-8994(98)00027-7
1998

Acute Swelling of the Cerebellum in Childhood
Journal of Child Neurology
Juliette Hukin and Douglas D. Cochrane and John U. Crichton
DOI: 10.1177/088307389701200411
06/1997

Basal ganglia infarction associated with HHV-6 infection.
Archives of Disease in Childhood
Webb DW and Bjornson BH and Sargent MA and Hukin J and Thomas EE
DOI: 10.1136/adc.76.4.362
PubMed: 9166034
04/1997

Long-term neurologic and psychomotor sequelae after neonatal tetanus
Journal of Child Neurology
Hukin, J. and Cochrane, D.D. and Crichton, J.U.
DOI: 10.1177/088307389701200410
1997

Reye syndrome associated with subclinical varicella zoster virus and influenza a infection
Pediatric Neurology
Juliette Hukin and Anne K. Junker and Eva E. Thomas and Kevin Farrell
DOI: 10.1016/0887-8994(93)90050-m
03/1993

Reye syndrome associated with subclinical varicella zoster virus and influenza a infection
Pediatric Neurology
Hukin, J. and Junker, A.K. and Thomas, E.E. and Farrell, K.
DOI: 10.1016/0887-8994(93)90050-M
1993

Research

Headstart III
Earlier generations of multi-center "Baby" protocols have demonstrated the feasibility of chemotherapy-only strategies for young children with newly diagnosed malignant brain tumors. The disease-free survivals attained with these regimens, however, were disappointing. The "Head Start I and II" studies demonstrated generally superior outcome for patients with medulloblastoma, other PNET and ependymoma than other such studies.

The primary aim of Headstart III is to determine the two year event-free survival and overall survival from time of study enrollment, for young children with medulloblastoma and other malignant tumours with induction chemotherapy followed by consolidation with myeloablative chemotherapy and autologous hematopoietic cell rescue, with the aim of avoiding, deferring or reducing radiation therapy to the developing brain. Early results are demonstrating favourable outcomes for certain patient groups. We are working on the next study which will be Head Start IV.

Longitudinal study evaluating the recurrence rate in childhood ependymoma
The purpose of this study is to report on the incidence of early and late recurrences in childhood ependymoma, their management and the success thereof, and to evaluate long-term functional status.