Sharon Dell

MD, FRCPC

Investigator, BC Children's Hospital
Head, Division of Respiratory Medicine, Department of Pediatrics, University of British Columbia
Professor, Department of Pediatrics, Faculty of Medicine, University of British Columbia

I am a health outcomes researcher in the field of children’s lung diseases. Combining clinical epidemiology training with classical population-based epidemiology & health services research methods, and collaborating with basic science researchers, has enabled me to study a number of clinically relevant issues in childhood asthma, primary ciliary dyskinesia (PCD) and interstitial lung disease (ILD). Early in my career, my main interest was to identify modifiable risk factors for childhood asthma. As my career progressed, I became interested in improving health outcomes for rare lung diseases in children, particularly PCD. I am a principal investigator in several multi-center clinical studies of children with PCD and ILD, with a particular interest in diagnostic test development & performance, health related quality of life measures, genotype-phenotype associations and clinical trials.

Academic Affiliations

  • Professor, Division of Respiratory Medicine, Department of Pediatrics, Faculty of Medicine, University of British Columbia
  • Research Theme: Evidence to Innovation
  • Research Group(s): Clinical Practice, Outcomes and Innovation; Clinical and Community Data, Analytics and Informatics; Origins of Child Health and Disease; Rare Diseases

Contact Information

Location

4480 Oak Street, Vancouver, British Columbia, Canada, V6H3V4

Hyperpolarized 129Xe MRI and Spectroscopy: Quantitative Measurements, Results, and Emerging Opportunities

Radiology: Cardiothoracic Imaging

Alexandra Schmidt and James A. Liggins and Haad Bhutta and Sharon D. Dell and Janice M. Leung and Don D. Sin and Jonathon A. Leipsic and Jonathan H. Rayment and Rachel L. Eddy

DOI: 10.1148/ryct.240562

08 / 2025

Repeatability of Multiple Breath Washout in Pediatric Primary Ciliary Dyskinesia

Pediatric Pulmonology

Wallace B. Wee and Layan M. Bashi and Renee Jensen and Jonathan H. Rayment and Teresa To and Felix Ratjen and Giles Santyr and Sharon D. Dell

DOI: 10.1002/ppul.71107

07 / 2025

Lung Function Recovery from Pulmonary Exacerbations Treated with Oral Antibiotics in Primary Ciliary Dyskinesia

Annals of the American Thoracic Society

Dvir Gatt and Michelle Shaw and Valerie Waters and Fiona Kritzinger and Melinda Solomon and Sharon Dell and Felix Ratjen

DOI: 10.1513/AnnalsATS.202407-771OC

05 / 2025

The Impact of Age of Diagnosis in Children with Primary Ciliary Dyskinesia

Annals of the American Thoracic Society

Dvir Gatt and Michelle Shaw and Fiona Kritzinger and Melinda Solomon and Sharon Dell and Felix Ratjen

DOI: 10.1513/AnnalsATS.202403-230OC

02 / 2025

Progression of Otologic and Nasal Symptoms in Primary Ciliary Dyskinesia Throughout Childhood

OTO Open

Isabelle Dagher and Adam J. Kimple and Thomas W. Ferkol and Scott D. Sagel and Sharon D. Dell and Carlos E. Milla and Lang Li and Feng-Chang Lin and Kelli M. Sullivan and Maimoona A. Zariwala and Michael R. Knowles and Margaret Rosenfeld and Margaret W. Leigh and Stephanie D. Davis

DOI: 10.1002/oto2.70079

01 / 2025

Comparison of Longitudinal Outcomes in Children with Primary Ciliary Dyskinesia and Cystic Fibrosis

Annals of the American Thoracic Society

BreAnna Kinghorn and Margaret Rosenfeld and Erin Sullivan and Frankline M. Onchiri and Marshall D. Brown and Rhonda Szczesniak and Thomas W. Ferkol and Scott D. Sagel and Sharon D. Dell and Carlos Milla and Adam J. Shapiro and Kelli M. Sullivan and Maimoona A. Zariwala and Jessica E. Pittman and Michael R. Knowles and Stephanie D. Davis and Margaret W. Leigh

DOI: 10.1513/AnnalsATS.202311-1008OC

12 / 2024

Mortality of Pediatric Surgical Lung Biopsies in Ontario, Canada, 2000"2019

Annals of the American Thoracic Society

Wallace B. Wee and Shane Shapera and Teresa To and Priscilla P. L. Chiu and Sharon D. Dell and Jolene H. Fisher

DOI: 10.1513/AnnalsATS.202304-306OC

05 / 2024

Disease Manifestations in Siblings with Primary Ciliary Dyskinesia

Annals of the American Thoracic Society

Dvir Gatt and Michelle Shaw and Jacob McCoy and Fiona Kritzinger and Melinda Solomon and Sharon Dell and Felix Ratjen

DOI: 10.1513/AnnalsATS.202308-747RL

01 / 2024

Efficacy of Antibiotic Eradication Therapy of Early Pseudomonas aeruginosa Infection in Children with Primary Ciliary Dyskinesia

Annals of the American Thoracic Society

Dvir Gatt and Michelle Shaw and Wallace Wee and Melinda Solomon and Sharon D. Dell and Felix Ratjen

DOI: 10.1513/AnnalsATS.202210-858OC

06 / 2023

Airway Disease in Children with Primary Ciliary Dyskinesia: Impact of Ciliary Ultrastructure Defect and Genotype

Annals of the American Thoracic Society

BreAnna Kinghorn and Margaret Rosenfeld and Erin Sullivan and Frankline Onchiri and Thomas W. Ferkol and Scott D. Sagel and Sharon D. Dell and Carlos Milla and Adam J. Shapiro and Kelli M. Sullivan and Maimoona A. Zariwala and Jessica E. Pittman and Federico Mollica and Harm A. W. M. Tiddens and Mariette Kemner-van de Corput and Michael R. Knowles and Stephanie D. Davis and Margaret W. Leigh

DOI: 10.1513/AnnalsATS.202206-524OC

04 / 2023

Laterality Defects in Primary Ciliary Dyskinesia: Relationship to Ultrastructural Defect or Genotype

Annals of the American Thoracic Society

Andrew T. Barber and Adam J. Shapiro and Stephanie D. Davis and Thomas W. Ferkol and Jeffrey J. Atkinson and Scott D. Sagel and Sharon D. Dell and Kenneth N. Olivier and Carlos E. Milla and Margaret Rosenfeld and Lang Li and Feng-Chang Lin and Kelli M. Sullivan and Nicole A. Capps and Maimoona A. Zariwala and Michael R. Knowles and Margaret W. Leigh

DOI: 10.1513/AnnalsATS.202206-487OC

03 / 2023

Airway Inflammation in Children with Primary Ciliary Dyskinesia

Annals of the American Thoracic Society

Scott D. Sagel and Oren Kupfer and Brandie D. Wagner and Stephanie D. Davis and Sharon D. Dell and Thomas W. Ferkol and Jordana E. Hoppe and Margaret Rosenfeld and Kelli M. Sullivan and Harm A. W. M. Tiddens and Michael R. Knowles and Margaret W. Leigh

DOI: 10.1513/AnnalsATS.202204-314OC

01 / 2023

Lower Airway Nitrogen Oxide Levels in Children with Primary Ciliary Dyskinesia Is Linked to Neutrophilic Inflammation

The Journal of Pediatrics

Hartmut Grasemann and Nancy McDonald and Xi Zhou Yuan and Sharon Dell and Valerie Waters and Felix Ratjen

DOI: 10.1016/j.jpeds.2022.01.040

05 / 2022

Going beyond the chest X-ray:Investigating laterality defects in primary ciliary dyskinesia

Pediatric Pulmonology

Wallace B. Wee and Kimberley R. Kaspy and Michael G. Sawras and Michael R. Knowles and Maimoona A. Zariwala and Margaret W. Leigh and Sharon D. Dell and Adam J. Shapiro

DOI: 10.1002/ppul.25853

05 / 2022

Development and Validation of an Algorithm for Quality Grading of Pediatric Spirometry: A Quality Improvement Initiative

Annals of the American Thoracic Society

Lucy Perrem and David Wilson and Sharon D. Dell and Felix Ratjen

DOI: 10.1513/AnnalsATS.202103-382QI

01 / 2022

Does exposure to air pollution increase the risk of acute care in young children with asthma? An Ontario, Canada study.

Environmental research

DOI: 10.1016/j.envres.2021.111302 PubMed: 34019894

05 / 2021

Rare broncho-pulmonary arterial fistula in a healthy 9-year-old girl.

BMJ case reports

DOI: 10.1136/bcr-2020-234865 PubMed: 33004353

10 / 2020

Super-Resolution Microscopy and FIB-SEM Imaging Reveal Parental Centriole-Derived, Hybrid Cilium in Mammalian Multiciliated Cells.

Developmental cell

DOI: 10.1016/j.devcel.2020.09.016 PubMed: 33038333

10 / 2020

A quantitative super-resolution imaging toolbox for diagnosis of motile ciliopathies

Science Translational Medicine

Liu, Z. and Nguyen, Q.P.H. and Guan, Q. and Albulescu, A. and Erdman, L. and Mahdaviyeh, Y. and Kang, J. and Ouyang, H. and Hegele, R.G. and Moraes, T. and Goldenberg, A. and Dell, S.D. and Mennella, V.

DOI: 10.1126/scitranslmed.aay0071

Nasal nitric oxide measurement in primary ciliary dyskinesia a technical paper on standardized testing protocols

Annals of the American Thoracic Society

Shapiro, A.J. and Dell, S.D. and Gaston, B. and O'Connor, M. and Marozkina, N. and Manion, M. and Hazucha, M.J. and Leigh, M.W.

DOI: 10.1513/AnnalsATS.201904-347OT

Methodologic guidance and expectations for the development and reporting of prediction models and causal inference studies

Annals of the American Thoracic Society

Harhay, M.O. and Au, D.H. and Dell, S.D. and Gould, M.K. and Redline, S. and Ryerson, C.J. and Cooke, C.R.

DOI: 10.1513/AnnalsATS.202002-141ED

Effect of asthma exacerbation during pregnancy in women with asthma: A population-based cohort study

European Respiratory Journal

Abdullah, K. and Zhu, J. and Gershon, A. and Dell, S. and To, T.

DOI: 10.1183/13993003.01335-2019

Early life exposure to air pollution and incidence of childhood asthma, allergic rhinitis and eczema

European Respiratory Journal

To, T. and Zhu, J. and Stieb, D. and Gray, N. and Fong, I. and Pinault, L. and Jerrett, M. and Robichaud, A. and Mnard, R. and van Donkelaar, A. and Martin, R.V. and Hystad, P. and Brook, J.R. and Dell, S.

DOI: 10.1183/13993003.00913-2019

Maternal Metabolic Complications in Pregnancy and Offspring Behavior Problems at 2Years of Age

Maternal and Child Health Journal

Krzeczkowski, J.E. and Lau, A. and Fitzpatrick, J. and Tamana, S. and Smithson, L. and de Souza, R. and Kozyrskyj, A.L. and Lefebvre, D. and Becker, A.B. and Subbarao, P. and Turvey, S.E. and Pei, J. and Schmidt, L.A. and Sears, M.R. and Van Lieshout, R.J. and Mandhane, P.J. and Subbarao, P. and Anand, S.S. and Azad, M. and Becker, A.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M. and Daley, D. and Dell, S. and Denburg, J.A. and Duan, Q. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R. and Holness, D.L. and Hystad, P. and Kobor, M.S. and Kollman, T.R. and Kozyrskyj, A.L. and Laprise, C. and Lou, W.Y.W. and Macri, J. and Mandhane, P.M. and Miller, G. and Moraes, T. and Par, P.D. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Sears, M.R. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S. and To, T.

DOI: 10.1007/s10995-018-2691-y

Validation of pediatric health-related quality of life instruments for primary ciliary dyskinesia (QOL-PCD)

Pediatric Pulmonology

Behan, L. and Leigh, M.W. and Dell, S.D. and Quittner, A.L. and Hogg, C. and Lucas, J.S.

DOI: 10.1002/ppul.24507

Prolidase deficiency diagnosed by whole exome sequencing in a child with pulmonary capillaritis

ERS Monograph

Rayment, J.H. and Jobling, R. and Bowdin, S. and Cutz, E. and Dell, S.D.

DOI: 10.1183/23120541.00205-2018

Primary ciliary dyskinesia: Longitudinal study of lung disease by ultrastructure defect and genotype

American Journal of Respiratory and Critical Care Medicine

Davis, S.D. and Rosenfeld, M. and Lee, H.-S. and Ferkol, T.W. and Sagel, S.D. and Dell, S.D. and Milla, C. and Pittman, J.E. and Shapiro, A.J. and Sullivan, K.M. and Nykamp, K.R. and Krischer, J.P. and Zariwala, M.A. and Knowles, M.R. and Leigh, M.W.

DOI: 10.1164/rccm.201803-0548OC

Pediatric asthma: An unmet need for more effective, focused treatments

Pediatric Allergy and Immunology

Papadopoulos, N.G. and ?ustovi?, A. and Cabana, M.D. and Dell, S.D. and Deschildre, A. and Hedlin, G. and Hossny, E. and Le Souf, P. and Matricardi, P.M. and Nieto, A. and Phipatanakul, W. and Pitrez, P.M. and Pohunek, P. and Gavornikova, M. and Jaumont, X. and Price, D.B.

DOI: 10.1111/pai.12990

ERS and ATS diagnostic guidelines for primary ciliary dyskinesia: similarities and differences in approach to diagnosis

European Respiratory Journal

Shoemark, A. and Dell, S. and Shapiro, A. and Lucas, J.S.

DOI: 10.1183/13993003.01066-2019

Understanding parent perceptions of healthy physical activity for their child with a chronic medical condition: A cross-sectional study

Paediatrics and Child Health (Canada)

McMullen, J.A. and McCrindle, B.W. and Dell, S.D. and Feldman, B.M. and Longmuir, P.E.

DOI: 10.1093/pch/pxy122

Treatment of rituximab-associated chronic CNS enterovirus using IVIg and fluoxetine

Neurology

Sham, L. and Bitnun, A. and Branson, H. and Hazrati, L.-N. and Dell, S.D. and Yeung, R.S.M. and Johnstone, J. and Yeh, E.A.

DOI: 10.1212/WNL.0000000000007468

Prenatal depression and birth mode sequentially mediate maternal education's influence on infant sleep duration

Sleep Medicine

Matenchuk, B.A. and Tamana, S.K. and Lou, W.Y.W. and Lefebvre, D.L. and Sears, M.R. and Becker, A.B. and Azad, M.B. and Moraes, T.J. and Turvey, S.E. and Subbarao, P. and Kozyrskyj, A.L. and Mandhane, P.J. and Subbarao, P. and Turvey, S.E. and Anand, S.S. and Azad, M.B. and Becker, A.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Kozyrskyj, A.L. and Laprise, C. and Lou, W.Y.W. and Macri, J. and Mandhane, P.J. and Miller, G. and Moraes, T.J. and Par, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Sears, M.R. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.1016/j.sleep.2019.01.015

AnnalSats: New developments and advice for authors

Annals of the American Thoracic Society

Lederer, D.J. and Au, D.H. and Cooke, C.R. and Dell, S.D. and Gould, M.K. and Redline, S. and Kotloff, R.M.

DOI: 10.1513/AnnalsATS.201902-143ED

Full-term neonatal respiratory distress and chronic lung disease

Pediatric Annals

Chowdhury, N. and Giles, B.L. and Dell, S.D.

DOI: 10.3928/19382359-20190328-01

58 - Pulmonary Involvement in the Systemic Inflammatory Diseases of Childhood

Kendig's Disorders of the Respiratory Tract in Children

Dell, S.D. and Schneider, R. and Yeung, R.S.M.

DOI: 10.1016/B978-0-323-44887-1.00058-4

Quantitative high-speed video profiling discriminates between DNAH11 and HYDIN variants of primary ciliary dyskinesia

American Journal of Respiratory and Critical Care Medicine

Chioccioli, M. and Feriani, L. and Nguyen, Q. and Kotar, J. and Dell, S.D. and Mennella, V. and Amirav, I. and Cicuta, P.

DOI: 10.1164/rccm.201812-2256LE

Evaluation of the pulmonary radioaerosol mucociliary clearance scan as an adjunctive test for the diagnosis of primary ciliary dyskinesia in children

Pediatric Pulmonology

Vali, R. and Ghandourah, H. and Charron, M. and Nezhad, K.V. and Omarkhail, Y. and Khazaee, A. and Shammas, A. and Dell, S.D.

DOI: 10.1002/ppul.24509

PKD1L1-related situs inversus associated with sideroblastic anemia

Clinical Genetics

Rodriguez, S. and Chaturvedi, R. and Blanchette, V. and Dell, S. and Axford, M. and Cada, M. and Dror, Y.

DOI: 10.1111/cge.13512

Procedure volume and mortality after surgical lung biopsy in interstitial lungdisease

The European respiratory journal

Fisher, J.H. and Shapera, S. and To, T. and Marras, T.K. and Gershon, A. and Dell, S.

DOI: 10.1183/13993003.01164-2018

Neighborhood material deprivation is associated with childhood asthma development: Analysis of prospective administrative data

Canadian Respiratory Journal

Simons, E. and Dell, S.D. and Moineddin, R. and To, T.

DOI: 10.1155/2019/6808206

Residential green space and pathways to term birth weight in the Canadian Healthy Infant Longitudinal Development (CHILD) Study

International Journal of Health Geographics

Cusack, L. and Sbihi, H. and Larkin, A. and Chow, A. and Brook, J.R. and Moraes, T. and Mandhane, P.J. and Becker, A.B. and Azad, M.B. and Subbarao, P. and Kozyrskyj, A. and Takaro, T.K. and Sears, M.R. and Turvey, S.E. and Hystad, P. and Subbarao, P. and Sears, M.R. and Anand, S.S. and Becker, A.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Kozyrskyj, A.L. and Laprise, C. and Lou, W.Y.W. and Macri, J. and Mandhane, P.J. and Miller, G. and Moraes, T.J. and Par, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.1186/s12942-018-0160-x

Association of exposure to formula in the hospital and subsequent infant feeding practices with gut microbiota and risk of overweight in the first year of life

JAMA Pediatrics

Forbes, J.D. and Azad, M.B. and Vehling, L. and Tun, H.M. and Konya, T.B. and Guttman, D.S. and Field, C.J. and Lefebvre, D. and Sears, M.R. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Moraes, T.J. and Subbarao, P. and Scott, J.A. and Kozyrskyj, A.L. and Anand, S.S. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Laprise, C. and Lou, W.Y.W. and Macri, J. and Miller, G. and Pare, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.1001/jamapediatrics.2018.1161

20-Year trends in severe childhood asthma outcomes: Hospitalizations and intensive care visits

Canadian Journal of Respiratory, Critical Care, and Sleep Medicine

Radhakrishnan, D. and Dell, S.D. and Guttmann, A. and Shariff, S.Z. and To, T.

DOI: 10.1080/24745332.2018.1474401

Improved diagnostic yield compared with targeted gene sequencing panels suggests a role for whole-genome sequencing as a first-tier genetic test

Genetics in Medicine

Lionel, A.C. and Costain, G. and Monfared, N. and Walker, S. and Reuter, M.S. and Hosseini, S.M. and Thiruvahindrapuram, B. and Merico, D. and Jobling, R. and Nalpathamkalam, T. and Pellecchia, G. and Sung, W.W.L. and Wang, Z. and Bikangaga, P. and Boelman, C. and Carter, M.T. and Cordeiro, D. and Cytrynbaum, C. and Dell, S.D. and Dhir, P. and Dowling, J.J. and Heon, E. and Hewson, S. and Hiraki, L. and Inbar-Feigenberg, M. and Klatt, R. and Kronick, J. and Laxer, R.M. and Licht, C. and MacDonald, H. and Mercimek-Andrews, S. and Mendoza-Londono, R. and Piscione, T. and Schneider, R. and Schulze, A. and Silverman, E. and Siriwardena, K. and Snead, O.C. and Sondheimer, N. and Sutherland, J. and Vincent, A. and Wasserman, J.D. and Weksberg, R. and Shuman, C. and Carew, C. and Szego, M.J. and Hayeems, R.Z. and Basran, R. and Stavropoulos, D.J. and Ray, P.N. and Bowdin, S. and Meyn, M.S. and Cohn, R.D. and Scherer, S.W. and Marshall, C.R.

DOI: 10.1038/gim.2017.119

Associations between neighborhood walkability and incident and ongoing asthma in children

Annals of the American Thoracic Society

Simons, E. and Dell, S.D. and Moineddin, R. and To, T.

DOI: 10.1513/AnnalsATS.201708-693OC

Patterns of allergic sensitization and atopic dermatitis from 1 to 3 years: Effects on allergic diseases

Clinical and Experimental Allergy

Dharma, C. and Lefebvre, D.L. and Tran, M.M. and Lou, W.Y.W. and Subbarao, P. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Sears, M.R. and Anand, S.S. and Azad, M.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Kozyrskyj, A.L. and Laprise, C. and Macri, J. and Miller, G. and Moraes, T.J. and Par, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.1111/cea.13063

Prediction of long-term neurodevelopmental outcome in preterm infants using trajectories of general movement assessments

Journal of Perinatology

van Dyk, J. and Church, P. and Dell, S. and To, T. and Luther, M. and Shah, V.

DOI: 10.1038/s41372-018-0173-0

Diagnosing atopic dermatitis in infancy: Questionnaire reports vs criteria-based assessment

Paediatric and Perinatal Epidemiology

Dharma, C. and Lefebvre, D.L. and Tran, M.M. and Lu, Z. and Lou, W.Y.W. and Subbarao, P. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Moraes, T.J. and Azad, M.B. and Sears, M.R. and Anand, S.S. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Kozyrskyj, A.L. and Laprise, C. and Macri, J. and Miller, G. and Par, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.1111/ppe.12525

Diagnosis of primary ciliary dyskinesia: An official American thoracic society clinical practice guideline

American Journal of Respiratory and Critical Care Medicine

Shapiro, A.J. and Davis, S.D. and Polineni, D. and Manion, M. and Rosenfeld, M. and Dell, S.D. and Chilvers, M.A. and Ferkol, T.W. and Zariwala, M.A. and Sagel, S.D. and Josephson, M. and Morgan, L. and Yilmaz, O. and Olivier, K.N. and Milla, C. and Pittman, J.E. and Leigh Anne Daniels, M. and Jones, M.H. and Janahi, I.A. and Ware, S.M. and Daniel, S.J. and Cooper, M.L. and Nogee, L.M. and Anton, B. and Eastvold, T. and Ehrne, L. and Guadagno, E. and Knowles, M.R. and Leigh, M.W. and Lavergne, V.

DOI: 10.1164/rccm.201805-0819ST

Predicting the atopic march: Results from the Canadian Healthy Infant Longitudinal Development Study

Journal of Allergy and Clinical Immunology

Tran, M.M. and Lefebvre, D.L. and Dharma, C. and Dai, D. and Lou, W.Y.W. and Subbarao, P. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Sears, M.R. and Subbarao, P. and Anand, S.S. and Azad, M. and Becker, A.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Kozyrskyj, A.L. and Laprise, C. and Lou, W.Y.W. and Macri, J. and Mandhane, P.J. and Miller, G. and Moraes, T.J. and Par, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Sears, M.R. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S. and To, T.

DOI: 10.1016/j.jaci.2017.08.024

Severe disease due to CCDC40 gene variants and the perils of late diagnosis in primary ciliary dyskinesia

BMJ Case Reports

Ghandourah, H. and Dell, S.D.

DOI: 10.1136/bcr-2018-224964

Parent-reported symptoms of sleep disordered breathing is associated with increased behavioral problems at 2 years of age: The Canadian Healthy Infant Longitudinal Development (CHILD) birth cohort study.

Sleep

DOI: 10.1093/sleep/zsx177 PubMed: 29099980

11 / 2017

Maternal depressive symptoms linked to reduced fecal Immunoglobulin A concentrations in infants.

Brain, behavior, and immunity

DOI: 10.1016/j.bbi.2017.10.007 PubMed: 29032226

10 / 2017

Concomitant diffuse alveolar hemorrhage and pulmonary embolism in a child with isolated pulmonary capillaritis

Annals of the American Thoracic Society

Rayment, J.H. and Cutz, E. and Levy, D.M. and Dell, S.D.

DOI: 10.1513/AnnalsATS.201610-783LE

Growth and nutritional status, and their association with lung function: a study from the international Primary Ciliary Dyskinesia Cohort

The European respiratory journal

Goutaki, M. and Halbeisen, F.S. and Spycher, B.D. and Maurer, E. and Belle, F. and Amirav, I. and Behan, L. and Boon, M. and Carr, S. and Casaulta, C. and Clement, A. and Crowley, S. and Dell, S. and Ferkol, T. and Haarman, E.G. and Karadag, B. and Knowles, M. and Koerner-Rettberg, C. and Leigh, M.W. and Loebinger, M.R. and Mazurek, H. and Morgan, L. and Nielsen, K.G. and Phillipsen, M. and Sagel, S.D. and Santamaria, F. and Schwerk, N. and Yiallouros, P. and Lucas, J.S. and Kuehni, C.E.

DOI: 10.1183/13993003.01659-2017

European Respiratory Society guidelines for the diagnosis of primary ciliary dyskinesia

European Respiratory Journal

Lucas, J.S. and Barbato, A. and Collins, S.A. and Goutaki, M. and Behan, L. and Caudri, D. and Dell, S. and Eber, E. and Escudier, E. and Hirst, R.A. and Hogg, C. and Jorissen, M. and Latzin, P. and Legendre, M. and Leigh, M.W. and Midulla, F. and Nielsen, K.G. and Omran, H. and Papon, J.-F. and Pohunek, P. and Redfern, B. and Rigau, D. and Rindlisbacher, B. and Santamaria, F. and Shoemark, A. and Snijders, D. and Tonia, T. and Titieni, A. and Walker, W.T. and Werner, C. and Bush, A. and Kuehni, C.E.

DOI: 10.1183/13993003.01090-2016

Recognition and management of severe asthma: A Canadian Thoracic Society position statement

Canadian Journal of Respiratory, Critical Care, and Sleep Medicine

FitzGerald, J.M. and Lemiere, C. and Lougheed, M.D. and Ducharme, F.M. and Dell, S.D. and Ramsey, C. and Yang, M.C.L. and Ct, A. and Watson, W. and Olivenstein, R. and Van Dam, A. and Villa-Roel, C. and Grad, R.

DOI: 10.1080/24745332.2017.1395250

Primary ciliary dyskinesia: Mechanisms and management

Application of Clinical Genetics

Damseh, N. and Quercia, N. and Rumman, N. and Dell, S.D. and Kim, R.H.

DOI: 10.2147/TACG.S127129

Tracheobronchomalacia in neonates: The "new Bronchopulmonary Dysplasia" is not just about the alveoli

Annals of the American Thoracic Society

Dell, S.D.

DOI: 10.1513/AnnalsATS.201706-507ED

In vivo immune signatures of healthy human pregnancy: Inherently inflammatory or anti-inflammatory?

PLoS ONE

Graham, C. and Chooniedass, R. and Stefura, W.P. and Becker, A.B. and Sears, M.R. and Turvey, S.E. and Mandhane, P.J. and Subbarao, P. and HayGlass, K.T. and Sears, M.R. and Subbarao, P. and Allen, R. and Anand, S.S. and Becker, A.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M. and Daley, D. and Dell, S. and Denburg, J.A. and Elliott, S. and Grasemann, H. and Hay-Glass, K. and Hegele, R. and Holness, D.L. and Lou, W.Y.W. and Kobor, M.S. and Kollman, T.R. and Kozyrskyj, A.A. and Laprise, C. and Larche, M. and Macri, J. and Mandhane, P.M. and Miller, G. and Moqbel, R. and Moraes, T. and Pare, P.D. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Takaro, T. and Tang, P. and Tebbutt, S. and To, T. and Turvey, S.E.

DOI: 10.1371/journal.pone.0177813

Cesarean section, formula feeding, and infant antibiotic exposure: Separate and combined impacts on gut microbial changes in later infancy

Frontiers in Pediatrics

Yasmin, F. and Tun, H.M. and Konya, T.B. and Guttman, D.S. and Chari, R.S. and Field, C.J. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Subbarao, P. and Sears, M.R. and Scott, J.A. and Dinu, I. and Kozyrskyj, A.L. and Anand, S.S. and Azad, M.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Laprise, C. and Lou, W.Y.W. and Macri, J. and Miller, G. and Moraes, T.J. and Par, P. and Ramsey, C. and Ratjen, F. and Sandford, A. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.3389/fped.2017.00200

Validation of a health-related quality of life instrument for primary ciliary dyskinesia (QOL-PCD)

Thorax

Behan, L. and Leigh, M.W. and Dell, S.D. and Dunn Galvin, A. and Quittner, A.L. and Lucas, J.S.

DOI: 10.1136/thoraxjnl-2016-209356

Misdiagnosis of asthma in schoolchildren

Pediatric Pulmonology

Yang, C.L. and Simons, E. and Foty, R.G. and Subbarao, P. and To, T. and Dell, S.D.

DOI: 10.1002/ppul.23541

Breastfeeding, maternal asthma and wheezing in the first year of life: A longitudinal birth cohort study

European Respiratory Journal

Azad, M.B. and Vehling, L. and Lu, Z. and Dai, D. and Subbarao, P. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Lefebvre, D.L. and Sears, M.R. and Anand, S.S. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M. and Daley, D. and Dell, S. and Denburg, J.A. and Duan, Q. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R. and Holness, D.L. and Hystad, P. and Lou, W.Y.W. and Kobor, M.S. and Kollman, T.R. and Kozyrskyj, A.L. and Laprise, C. and Macri, J. and Mandhane, P.M. and Miller, G. and Moraes, T. and Par, P.D. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S. and To, T. and Turvey, S.E.

DOI: 10.1183/13993003.02019-2016

The PD20 but not the PC20 in a methacholine challenge test is device independent

Annals of Allergy, Asthma and Immunology

Coates, A.L. and Dell, S.D. and Cockcroft, D.W. and Gauvreau, G.M.

DOI: 10.1016/j.anai.2017.01.010

Pulmonary interstitial glycogenosis associated with a spectrum of neonatal pulmonary disorders

Human Pathology

Cutz, E. and Chami, R. and Dell, S. and Langer, J. and Manson, D.

DOI: 10.1016/j.humpath.2017.06.026

Exposure to household furry pets influences the gut microbiota of infants at 3-4 months following various birth scenarios

Microbiome

Tun, H.M. and Konya, T. and Takaro, T.K. and Brook, J.R. and Chari, R. and Field, C.J. and Guttman, D.S. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Subbarao, P. and Sears, M.R. and Scott, J.A. and Kozyrskyj, A.L. and Anand, S.S. and Cyr, M. and Denburg, J.A. and Macri, J. and Eiwegger, T. and Azad, M. and HayGlass, K. and Ramsey, C. and Simons, E. and Befus, A.D. and Brauer, M. and Daley, D. and Kobor, M.S. and Kollmann, T.R. and Par, P.D. and Sandford, A. and Tebbutt, S. and Holness, D.L. and Lou, W.Y.W. and Scott, J. and Silverman, F. and Chen, E. and Miller, G. and Dell, S. and Grasemann, H. and Hegele, R. and Moraes, T. and Ratjen, F. and To, T. and Duan, Q. and Hystad, P. and Laprise, C. and Takaro, T.

DOI: 10.1186/s40168-017-0254-x

Timing of food introduction and development of food sensitization in a prospective birth cohort

Pediatric Allergy and Immunology

Tran, M.M. and Lefebvre, D.L. and Dai, D. and Dharma, C. and Subbarao, P. and Lou, W. and Azad, M.B. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Sears, M.R. and Anand, S.S. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M.M. and Daley, D. and Dell, S.D. and Denburg, J.A. and Duan, Q.L. and Eiwegger, T. and Grasemann, H. and HayGlass, K. and Hegele, R.G. and Holness, D.L. and Hystad, P. and Kobor, M. and Kollmann, T.R. and Kozyrskyj, A.L. and Laprise, C. and Miller, G. and Moraes, T.J. and Par, P. and Ramsey, C. and Ratjen, F. and andford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Simons, E. and Takaro, T. and Tebbutt, S.J. and To, T.

DOI: 10.1111/pai.12739

Modes of Infant Feeding and the Risk of Childhood Asthma: A Prospective Birth Cohort Study

Journal of Pediatrics

Klopp, A. and Vehling, L. and Becker, A.B. and Subbarao, P. and Mandhane, P.J. and Turvey, S. and Lefebvre, D.L. and Sears, M.R. and Daley, D. and Silverman, F. and Hayglass, K. and Kobor, M. and Kollmann, T. and Brook, J. and Ramsey, C. and Macri, J. and Sandford, A. and Pare, P. and Tebbutt, S. and Brauer, M. and Denburg, J. and Cyr, M. and Kozyrskyj, A. and Becker, A. and Chen, E. and Takaro, T. and Ratjen, F. and Grasemann, H. and Dell, S. and To, T. and Moraes, T. and Subbarao, P. and Holness, L. and Befus, A.D. and Mandhane, P. and Laprise, C. and Scott, J. and Hegele, R. and Lou, W. and Anand, S. and Sears, M. and Simons, E. and Azad, M. and Eiwegger, T. and Duan, Q. and Hystad, P. and Scott, J. and Azad, M.B.

DOI: 10.1016/j.jpeds.2017.07.012

High fecal IgA is associated with reduced Clostridium difficile colonization in infants.

Microbes and infection

DOI: 10.1016/j.micinf.2016.05.001 PubMed: 27235197

09 / 2016

Cognitive Enhancement in Infants Associated with Increased Maternal Fruit Intake During Pregnancy: Results from a Birth Cohort Study with Validation in an Animal Model.

EBioMedicine

DOI: 10.1016/j.ebiom.2016.04.025 PubMed: 27428442

06 / 2016

Impact of maternal intrapartum antibiotics, method of birth and breastfeeding on gut microbiota during the first year of life: a prospective cohort study.

BJOG : an international journal of obstetrics and gynaecology

DOI: 10.1111/1471-0528.13601 PubMed: 26412384

05 / 2016

Pulmonary Alveolar Microlithiasis

Canadian Respiratory Journal

Mehta, K. and Dell, S. and Birken, C. and Al-Saleh, S.

DOI: 10.1155/2016/4938632

Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art review

Pediatric Pulmonology

Shapiro, A.J. and Zariwala, M.A. and Ferkol, T. and Davis, S.D. and Sagel, S.D. and Dell, S.D. and Rosenfeld, M. and Olivier, K.N. and Milla, C. and Daniel, S.J. and Kimple, A.J. and Manion, M. and Knowles, M.R. and Leigh, M.W.

DOI: 10.1002/ppul.23304

Changes in airway inflammation during pulmonary exacerbations in patients with cystic fibrosis and primary ciliary dyskinesia

European Respiratory Journal

Ratjen, F. and Waters, V. and Klingel, M. and McDonald, N. and Dell, S. and Leahy, T.R. and Yau, Y. and Grasemann, H.

DOI: 10.1183/13993003.01390-2015

Frequency of health service use in the year prior to asthma death

Journal of Asthma

To, T. and Zhu, J. and Williams, D.P. and Feldman, L. and Simatovic, J. and Gershon, A. and Lougheed, M.D. and Licskai, C. and Dell, S.

DOI: 10.3109/02770903.2015.1064949

Primary ciliary dyskinesia: First health-related quality-of-life measures for pediatric patients

Annals of the American Thoracic Society

Dell, S.D. and Leigh, M.W. and Lucas, J.S. and Ferkol, T.W. and Knowles, M.R. and Alpern, A. and Behan, L. and Morris, A.M. and Hogg, C. and Galvin, A.D. and Quittner, A.L.

DOI: 10.1513/AnnalsATS.201603-198OC

Clinical features and associated likelihood of primary ciliary dyskinesia in children and adolescents

Annals of the American Thoracic Society

Leigh, M.W. and Ferkol, T.W. and Davis, S.D. and Lee, H.-S. and Rosenfeld, M. and Dell, S.D. and Sagel, S.D. and Milla, C. and Olivier, K.N. and Sullivan, K.M. and Zariwala, M.A. and Pittman, J.E. and Shapiro, A.J. and Carson, J.L. and Krischer, J. and Hazucha, M.J. and Knowles, M.R.

DOI: 10.1513/AnnalsATS.201511-748OC

Association between artificially sweetened beverage consumption during pregnancy and infant body mass index

JAMA Pediatrics

Azad, M.B. and Sharma, A.K. and De Souza, R.J. and Dolinsky, V.W. and Becker, A.B. and Mandhane, P.J. and Turvey, S.E. and Subbarao, P. and Lefebvre, D.L. and Sears, M.R. and Anand, S. and Cyr, M. and Denburg, J.A. and Larch, M. and Macri, J. and Dell, S. and Grasemann, H. and Hegele, R. and Moraes, T.J. and Ratjen, F. and To, T. and Allen, R. and Takaro, T.K. and HayGlass, K.T. and Moqbel, R. and Ramsey, C. and Simons, E. and Befus, A.D. and Kozyrskyj, A.L. and Brauer, M. and Daley, D. and Kobor, M.S. and Kollmann, T.R. and Par, P.D. and Sandford, A. and Tang, P. and Tebbutt, S. and Brook, J.R. and Holness, D.L. and Wendy Lou, W.Y. and Scott, J. and Scott, J.A. and Silverman, F. and Chen, E. and Miller, G.E. and Elliott, S. and Laprise, C.

DOI: 10.1001/jamapediatrics.2016.0301

Treatment recommendations in Primary Ciliary Dyskinesia

Paediatric Respiratory Reviews

Polineni, D. and Davis, S.D. and Dell, S.D.

DOI: 10.1016/j.prrv.2015.10.002

The annual September peak in asthma exacerbation rates still a reality?

Annals of the American Thoracic Society

Larsen, K. and Zhu, J. and Feldman, L.Y. and Simatovic, J. and Dell, S. and Gershon, A.S. and To, T.

DOI: 10.1513/AnnalsATS.201508-545OC

Clinical manifestations in primary ciliary dyskinesia: Systematic review and meta-analysis

European Respiratory Journal

Goutaki, M. and Meier, A.B. and Halbeisen, F.S. and Lucas, J.S. and Dell, S.D. and Maurer, E. and Casaulta, C. and Jurca, M. and Spycher, B.D. and Kuehni, C.E.

DOI: 10.1183/13993003.00736-2016

ATS core curriculum 2016: Part III. Pediatric pulmonary medicine

Annals of the American Thoracic Society

Boyer, D. and Thomson, C.C. and Cohen, R. and Rao, D. and Dell, S. and Rayment, J. and Wang, R. and Dy, F.J. and Wambach, J. and Tam-Williams, J. and Simon, D. and Price, E. and Oermann, C.M. and Singh, A. and Rettig, J.S. and Duncan, E.D. and Baker, C.D. and Liptzin, D.R. and Moore, P.E.

DOI: 10.1513/AnnalsATS.201602-097CME

Infant gut immunity: A preliminary study of IgA associations with breastfeeding

Journal of Developmental Origins of Health and Disease

Bridgman, S.L. and Konya, T. and Azad, M.B. and Sears, M.R. and Becker, A.B. and Turvey, S.E. and Mandhane, P.J. and Subbarao, P. and Sears, M.R. and Subbarao, P. and Allen, R. and Anand, S.S. and Becker, A.B. and Befus, A.D. and Brauer, M. and Brook, J.R. and Chen, E. and Cyr, M. and Daley, D. and Dell, S. and Denburg, J.A. and Elliott, S. and Grasemann, H. and HayGlass, K. and Hegele, R. and Holness, D.L. and Lou, W.Y.W. and Kobor, M.S. and Kollman, T.R. and Kozyrskyj, A.L. and Laprise, C. and Larch, M. and MacRi, J. and Mandhane, P.M. and Miller, G. and Moqbel, R. and Moraes, T. and Par, P.D. and Ramsey, C. and Ratjen, F. and Sandford, A. and Scott, J.A. and Scott, J. and Silverman, F. and Takaro, T. and Tang, P. and Tebbutt, S. and To, T. and Scott, J.A. and Field, C.J. and Kozyrskyj, A.L.

DOI: 10.1017/S2040174415007862

The Canadian Healthy Infant Longitudinal Development (CHILD) Study: examining developmental origins of allergy and asthma.

Thorax

DOI: 10.1136/thoraxjnl-2015-207246 PubMed: 26069286

10 / 2015

Perinatal antibiotic exposure of neonates in Canada and associated risk factors: a population-based study.

The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal Obstetricians

DOI: 10.3109/14767058.2014.947578 PubMed: 25053193

07 / 2015

The Canadian healthy infant longitudinal development birth cohort study: biological samples and biobanking.

Paediatric and perinatal epidemiology

DOI: 10.1111/ppe.12161 PubMed: 25405552

01 / 2015

Clinical features of childhood primary ciliary dyskinesia by genotype and ultrastructural phenotype

American Journal of Respiratory and Critical Care Medicine

Davis, S.D. and Ferkol, T.W. and Rosenfeld, M. and Lee, H.-S. and Dell, S.D. and Sagel, S.D. and Milla, C. and Zariwala, M.A. and Pittman, J.E. and Shapiro, A.J. and Carson, J.L. and Krischer, J.P. and Hazucha, M.J. and Cooper, M.L. and Knowles, M.R. and Leigh, M.W.

DOI: 10.1164/rccm.201409-1672OC

Whole-exome sequencing and targeted copy number analysis in primary ciliary dyskinesia

G3: Genes, Genomes, Genetics

Marshall, C.R. and Scherer, S.W. and Zariwala, M.A. and Lau, L. and Paton, T.A. and Stockley, T. and Jobling, R.K. and Ray, P.N. and Knowles, M.R. and Hall, D.A. and Dell, S.D. and Kim, R.H.

DOI: 10.1534/g3.115.019851

The Canadian Healthy Infant Longitudinal Development (CHILD) birth cohort study: assessment of environmental exposures.

Journal of exposure science & environmental epidemiology

DOI: 10.1038/jes.2015.7 PubMed: 25805254

Serum Krebs Von Den Lungen-6 as a Biomarker for Early Detection of Bronchiolitis Obliterans Syndrome in Children Undergoing Allogeneic Stem Cell Transplantation

Biology of Blood and Marrow Transplantation

Gassas, A. and Schechter, T. and Krueger, J. and Craig-Barnes, H. and Sung, L. and Ali, M. and Dell, S. and Egeler, R.M. and Zaidman, I. and Palaniyar, N.

DOI: 10.1016/j.bbmt.2015.04.021

Prediction of childhood atopy by questionnaire

Clinical and Experimental Allergy

Simons, E. and Kwon, S. and Yang, C. and Dell, S.D.

DOI: 10.1111/cea.12510

Diffuse lung disease in biopsied children 2 to 18 years of age application of the chILD classification scheme

Annals of the American Thoracic Society

Fan, L.L. and Dishop, M.K. and Galambos, C. and Askin, F.B. and White, F.V. and Langston, C. and Liptzin, D.R. and Kroehl, M.E. and Deutsch, G.H. and Young, L.R. and Kurland, G. and Hagood, J. and Dell, S. and Trapnell, B.C. and Deterding, R.R.

DOI: 10.1513/AnnalsATS.201501-064OC

Diagnosis and management of asthma in preschoolers: A Canadian Thoracic Society and Canadian Pediatric Society position paper,Le diagnostic et la prise en charge de l'asthme chez les enfants d'ge prscolaire : Document de principes la Socit canadienne de thoracologie et la Socit canadienne de pdiatrie

Paediatrics and Child Health (Canada)

Ducharme, F.M. and Dell, S.D. and Radhakrishnan, D. and Grad, R.M. and Watson, W.T.A. and Yang, C.L. and Zelman, M.

DOI: 10.1093/pch/20.7.362

Spatial analysis of exposure to traffic-related air pollution at birth and childhood atopic asthma in Toronto, Ontario

Health and Place

Shankardass, K. and Jerrett, M. and Dell, S.D. and Foty, R. and Stieb, D.

DOI: 10.1016/j.healthplace.2015.06.001

Erratum: Association among fraction of exhaled nitrous oxide, bronchodilator response and inhaled corticosteroid type (Canadian Respiratory Journal (2015) 22:3 (153-156))

Canadian Respiratory Journal

Smith, R.W. and Downey, K. and Snow, N. and Dell, S. and Smith, W.G.

Provocative dose of methacholine causing a 20% drop in FEV1 should be used to interpret methacholine challenge tests with modern nebulizers

Annals of the American Thoracic Society

Dell, S.D. and Bola, S.S. and Foty, R.G. and Marshall, L.C. and Nelligan, K.A. and Coates, A.L.

DOI: 10.1513/AnnalsATS.201409-433OC

Health risk of air pollution on people living with major chronic diseases: A Canadian population-based study

BMJ Open

To, T. and Feldman, L. and Simatovic, J. and Gershon, A.S. and Dell, S. and Su, J. and Foty, R. and Licskai, C.

DOI: 10.1136/bmjopen-2015-009075

COPA mutations impair ER-Golgi transport and cause hereditary autoimmune-mediated lung disease and arthritis

Nature Genetics

Watkin, L.B. and Jessen, B. and Wiszniewski, W. and Vece, T.J. and Jan, M. and Sha, Y. and Thamsen, M. and Santos-Cortez, R.L.P. and Lee, K. and Gambin, T. and Forbes, L.R. and Law, C.S. and Stray-Pedersen, A. and Cheng, M.H. and Mace, E.M. and Anderson, M.S. and Liu, D. and Tang, L.F. and Nicholas, S.K. and Nahmod, K. and Makedonas, G. and Canter, D.L. and Kwok, P.-Y. and Hicks, J. and Jones, K.D. and Penney, S. and Jhangiani, S.N. and Rosenblum, M.D. and Dell, S.D. and Waterfield, M.R. and Papa, F.R. and Muzny, D.M. and Zaitlen, N. and Leal, S.M. and Gonzaga-Jauregui, C. and Boerwinkle, E. and Eissa, N.T. and Gibbs, R.A. and Lupski, J.R. and Orange, J.S. and Shum, A.K.

DOI: 10.1038/ng.3279

Bleomycin-associated lung toxicity in childhood cancer survivors

Journal of Pediatric Hematology/Oncology

Zorzi, A.P. and Yang, C.L. and Dell, S. and Nathan, P.C.

Infant gut microbiota and food sensitization: Associations in the first year of life

Clinical and Experimental Allergy

Azad, M.B. and Konya, T. and Guttman, D.S. and Field, C.J. and Sears, M.R. and Hayglass, K.T. and Mandhane, P.J. and Turvey, S.E. and Subbarao, P. and Becker, A.B. and Scott, J.A. and Kozyrskyj, A.L. and Allen, R. and Befus, D. and Brauer, M. and Brook, J. and Cyr, M. and Chen, E. and Daley, D. and Dell, S. and Denburg, J. and Elliott, S. and Grasemann, H. and Hegele, R. and Holness, L. and Kobor, M. and Kollmann, T. and Laprise, C. and Larch, M. and Lou, W. and Macri, J. and Miller, G. and Moqbel, R. and Moraes, T. and Par, P. and Ramsey, C. and Ratjen, F. and Ritchie, B. and Sandford, A. and Scott, J. and Silverman, F. and Tebbutt, S. and Takaro, T. and Tang, P. and To, T.

DOI: 10.1111/cea.12487

Diagnosis and management of asthma in preschoolers: A Canadian Thoracic Society and Canadian Paediatric Society position paper

Paediatrics and Child Health (Canada)

Ducharme, F.M. and Dell, S.D. and Radhakrishnan, D. and Grad, R.M. and Watson, W.T.A. and Yang, C.L. and Zelman, M.

Parents and adolescents preferences for asthma control: A best-worst scaling choice experiment using an orthogonal main effects design

BMC Pulmonary Medicine

Ungar, W.J. and Hadioonzadeh, A. and Najafzadeh, M. and Tsao, N.W. and Dell, S. and Lynd, L.D.

DOI: 10.1186/s12890-015-0141-9

Association among fraction of exhaled nitrous oxide, bronchodilator response and inhaled corticosteroid type

Canadian Respiratory Journal

Smith, R.W. and Downey, K. and Snow, N. and Dell, S. and Smith, W.G.

Erratum: Diagnosis and management of asthma in preschoolers: A Canadian Thoracic Society and Canadian Paediatric Society position paper. (Can Respir J 2015;22(3) (135-143))

Canadian Respiratory Journal

Ducharme, F.M. and Dell, S.D. and Radhakrishnan, D.

Primary ciliary dyskinesia and neonatal respiratory distress

Pediatrics

Mullowney, T. and Manson, D. and Kim, R. and Stephens, D. and Shah, V. and Dell, S.

DOI: 10.1542/peds.2014-0808

Presence of other allergic disease modifies the effect of early childhood traffic-related air pollution exposure on asthma prevalence

Environment International

Dell, S.D. and Jerrett, M. and Beckerman, B. and Brook, J.R. and Foty, R.G. and Gilbert, N.L. and Marshall, L. and Miller, J.D. and To, T. and Walter, S.D. and Stieb, D.M.

DOI: 10.1016/j.envint.2014.01.002

Associations between bacterial communities of house dust and infant gut

Environmental Research

Konya, T. and Koster, B. and Maughan, H. and Escobar, M. and Azad, M.B. and Guttman, D.S. and Sears, M.R. and Becker, A.B. and Brook, J.R. and Takaro, T.K. and Kozyrskyj, A.L. and Scott, J.A. and Allen, R. and Befus, D. and Brauer, M. and Cyr, M. and Chen, E. and Daley, D. and Dell, S. and Denburg, J. and Elliott, S. and Grasemann, H. and HayGlass, K. and Hegele, R. and Holness, L. and Kobor, M. and Kollmann, T. and Laprise, C. and Larch, M. and Lou, W. and Macri, J. and Mandhane, P. and Miller, G. and Moqbel, R. and Moraes, T. and Par, P. and Ramsey, C. and Ratjen, F. and Ritchie, B. and Sandford, A. and Scott, J. and Silverman, F. and Subbarao, P. and Tebbutt, S. and Tang, P. and To, T. and Turvey, S.

DOI: 10.1016/j.envres.2014.02.005

The role of molecular genetic analysis in the diagnosis of primary ciliary dyskinesia

Annals of the American Thoracic Society

Kim, R.H. and Hall, D.A. and Cutz, E. and Knowles, M.R. and Nelligan, K.A. and Nykamp, K. and Zariwala, M.A. and Dell, S.D.

DOI: 10.1513/AnnalsATS.201306-194OC

Maternal second-hand smoke exposure in pregnancy is associated with childhood asthma development

Journal of Allergy and Clinical Immunology: In Practice

Simons, E. and To, T. and Moineddin, R. and Stieb, D. and Dell, S.D.

DOI: 10.1016/j.jaip.2013.11.014

Asthma deaths in a large provincial health system: A 10-year population-based study

Annals of the American Thoracic Society

To, T. and Simatovic, J. and Zhu, J. and Feldman, L. and Dell, S.D. and Lougheed, M.D. and Licskai, C. and Gershon, A.

DOI: 10.1513/AnnalsATS.201404-138OC

Laterality defects other than situs inversus totalis in primary ciliary dyskinesia: Insights into situs ambiguus and heterotaxy

Chest

Shapiro, A.J. and Davis, S.D. and Ferkol, T. and Dell, S.D. and Rosenfeld, M. and Olivier, K.N. and Sagel, S.D. and Milla, C. and Zariwala, M.A. and Wolf, W. and Carson, J.L. and Hazucha, M.J. and Burns, K. and Robinson, B. and Knowles, M.R. and Leigh, M.W.

DOI: 10.1378/chest.13-1704

Trends in the age of diagnosis of childhood asthma

Journal of Allergy and Clinical Immunology

Radhakrishnan, D.K. and Dell, S.D. and Guttmann, A. and Shariff, S.Z. and Liu, K. and To, T.

DOI: 10.1016/j.jaci.2014.05.012

Quantifying preferences for asthma control in parents and adolescents using best-worst scaling

Respiratory Medicine

Ungar, W.J. and Hadioonzadeh, A. and Najafzadeh, M. and Tsao, N.W. and Dell, S. and Lynd, L.D.

DOI: 10.1016/j.rmed.2014.03.014

Mutations in RSPH1 cause primary ciliary dyskinesia with a unique clinical and ciliary phenotype

American Journal of Respiratory and Critical Care Medicine

Knowles, M.R. and Ostrowski, L.E. and Leigh, M.W. and Sears, P.R. and Davis, S.D. and Wolf, W.E. and Hazucha, M.J. and Carson, J.L. and Olivier, K.N. and Sagel, S.D. and Rosenfeld, M. and Ferkol, T.W. and Dell, S.D. and Milla, C.E. and Randell, S.H. and Yin, W. and Sannuti, A. and Metjian, H.M. and Noone, P.G. and Noone, P.J. and Olson, C.A. and Patrone, M.V. and Dang, H. and Lee, H.-S. and Hurd, T.W. and Gee, H.Y. and Otto, E.A. and Halbritter, J. and Kohl, S. and Kircher, M. and Krischer, J. and Bamshad, M.J. and Nickerson, D.A. and Hildebrandt, F. and Shendure, J. and Zariwala, M.A.

DOI: 10.1164/rccm.201311-2047OC

Developing alternative delivery systems for methacholine challenge tests

Journal of Aerosol Medicine and Pulmonary Drug Delivery

Coates, A.L. and Leung, K. and Dell, S.D.

DOI: 10.1089/jamp.2013.1036

Tachypnea of infancy as the first sign of Sanfilippo syndrome

Pediatrics

Chiang, J. and Raiman, J. and Cutz, E. and Solomon, M. and Dell, S.

DOI: 10.1542/peds.2013-2765

Gut microbiota of healthy Canadian infants: profiles by mode of delivery and infant diet at 4 months.

CMAJ : Canadian Medical Association Journal

DOI: 10.1503/cmaj.121189 PubMed: 23401405

03 / 2013

Chest health surveillance utility in the early detection of bronchiolitis obliterans syndrome in children after allo-SCT

Bone Marrow Transplantation

Gassas, A. and Craig-Barnes, H. and Dell, S. and Doyle, J. and Schechter, T. and Sung, L. and Egeler, M. and Palaniyar, N.

DOI: 10.1038/bmt.2012.228

Mutations in SPAG1 cause primary ciliary dyskinesia associated with defective outer and inner dynein arms

American Journal of Human Genetics

Knowles, M.R. and Ostrowski, L.E. and Loges, N.T. and Hurd, T. and Leigh, M.W. and Huang, L. and Wolf, W.E. and Carson, J.L. and Hazucha, M.J. and Yin, W. and Davis, S.D. and Dell, S.D. and Ferkol, T.W. and Sagel, S.D. and Olivier, K.N. and Jahnke, C. and Olbrich, H. and Werner, C. and Raidt, J. and Wallmeier, J. and Pennekamp, P. and Dougherty, G.W. and Hjeij, R. and Gee, H.Y. and Otto, E.A. and Halbritter, J. and Chaki, M. and Diaz, K.A. and Braun, D.A. and Porath, J.D. and Schueler, M. and Baktai, G. and Griese, M. and Turner, E.H. and Lewis, A.P. and Bamshad, M.J. and Nickerson, D.A. and Hildebrandt, F. and Shendure, J. and Omran, H. and Zariwala, M.A.

DOI: 10.1016/j.ajhg.2013.07.025

Children with Asthma Are Less Likely to Walk to School

Pediatric, Allergy, Immunology, and Pulmonology

Foty, R.G. and Nelligan, K. and To, T. and Stieb, D.M. and Dell, S.D.

DOI: 10.1089/ped.2012.0203

An official american thoracic society clinical practice guideline: Classification, evaluation, and management of childhood interstitial lung disease in infancy

American Journal of Respiratory and Critical Care Medicine

Kurland, G. and Deterding, R.R. and Hagood, J.S. and Young, L.R. and Brody, A.S. and Castile, R.G. and Dell, S. and Fan, L.L. and Hamvas, A. and Hilman, B.C. and Langston, C. and Nogee, L.M. and Redding, G.J.

DOI: 10.1164/rccm.201305-0923ST

ZMYND10 is mutated in primary ciliary dyskinesia and interacts with LRRC6

American Journal of Human Genetics

Zariwala, M.A. and Gee, H.Y. and Kurkowiak, M. and Al-Mutairi, D.A. and Leigh, M.W. and Hurd, T.W. and Hjeij, R. and Dell, S.D. and Chaki, M. and Dougherty, G.W. and Adan, M. and Spear, P.C. and Esteve-Rudd, J. and Loges, N.T. and Rosenfeld, M. and Diaz, K.A. and Olbrich, H. and Wolf, W.E. and Sheridan, E. and Batten, T.F.C. and Halbritter, J. and Porath, J.D. and Kohl, S. and Lovric, S. and Hwang, D.-Y. and Pittman, J.E. and Burns, K.A. and Ferkol, T.W. and Sagel, S.D. and Olivier, K.N. and Morgan, L.C. and Werner, C. and Raidt, J. and Pennekamp, P. and Sun, Z. and Zhou, W. and Airik, R. and Natarajan, S. and Allen, S.J. and Amirav, I. and Wieczorek, D. and Landwehr, K. and Nielsen, K. and Schwerk, N. and Sertic, J. and Khler, G. and Washburn, J. and Levy, S. and Fan, S. and Koerner-Rettberg, C. and Amselem, S. and Williams, D.S. and Mitchell, B.J. and Drummond, I.A. and Otto, E.A. and Omran, H. and Knowles, M.R. and Hildebrandt, F.

DOI: 10.1016/j.ajhg.2013.06.007

Founder mutation in RSPH4A identified in patients of hispanic descent with primary ciliary dyskinesia

Human Mutation

Daniels, M.L.A. and Leigh, M.W. and Davis, S.D. and Armstrong, M.C. and Carson, J.L. and Hazucha, M. and Dell, S.D. and Eriksson, M. and Collins, F.S. and Knowles, M.R. and Zariwala, M.A.

DOI: 10.1002/humu.22371

Zebrafish ciliopathy screen plus human mutational analysis identifies C21orf59 and CCDC65 defects as causing primary ciliary dyskinesia

American Journal of Human Genetics

Austin-Tse, C. and Halbritter, J. and Zariwala, M.A. and Gilberti, R.M. and Gee, H.Y. and Hellman, N. and Pathak, N. and Liu, Y. and Panizzi, J.R. and Patel-King, R.S. and Tritschler, D. and Bower, R. and O'Toole, E. and Porath, J.D. and Hurd, T.W. and Chaki, M. and Diaz, K.A. and Kohl, S. and Lovric, S. and Hwang, D.-Y. and Braun, D.A. and Schueler, M. and Airik, R. and Otto, E.A. and Leigh, M.W. and Noone, P.G. and Carson, J.L. and Davis, S.D. and Pittman, J.E. and Ferkol, T.W. and Atkinson, J.J. and Olivier, K.N. and Sagel, S.D. and Dell, S.D. and Rosenfeld, M. and Milla, C.E. and Loges, N.T. and Omran, H. and Porter, M.E. and King, S.M. and Knowles, M.R. and Drummond, I.A. and Hildebrandt, F.

DOI: 10.1016/j.ajhg.2013.08.015

Exome sequencing identifies mutations in CCDC114 as a cause of primary ciliary dyskinesia

American Journal of Human Genetics

Knowles, M.R. and Leigh, M.W. and Ostrowski, L.E. and Huang, L. and Carson, J.L. and Hazucha, M.J. and Yin, W. and Berg, J.S. and Davis, S.D. and Dell, S.D. and Ferkol, T.W. and Rosenfeld, M. and Sagel, S.D. and Milla, C.E. and Olivier, K.N. and Turner, E.H. and Lewis, A.P. and Bamshad, M.J. and Nickerson, D.A. and Shendure, J. and Zariwala, M.A.

DOI: 10.1016/j.ajhg.2012.11.003

Standardizing nasal nitric oxide measurement as a test for primary ciliary dyskinesia

Annals of the American Thoracic Society

Leigh, M.W. and Hazucha, M.J. and Chawla, K.K. and Baker, B.R. and Shapiro, A.J. and Brown, D.E. and Lavange, L.M. and Horton, B.J. and Qaqish, B. and Carson, J.L. and Davis, S.D. and Dell, S.D. and Ferkol, T.W. and Atkinson, J.J. and Olivier, K.N. and Sagel, S.D. and Rosenfeld, M. and Milla, C. and Lee, H.-S. and Krischer, J. and Zariwala, M.A. and Knowles, M.R.

DOI: 10.1513/AnnalsATS.201305-110OC

Severe lung injury and lung biopsy in children post-hematopoietic stem cell transplantation: The differences between allogeneic and autologous transplantation

Pediatric Transplantation

Gassas, A. and Craig-Barnes, H. and Dell, S.D. and Cox, P. and Schechter, T. and Doyle, J. and Sung, L. and Egeler, M. and Palaniyar, N.

DOI: 10.1111/petr.12060

A new exposure metric for traffic-related air pollution? An analysis of determinants of hopanes in settled indoor house dust

Environmental Health: A Global Access Science Source

Sbihi, H. and Brook, J.R. and Allen, R.W. and Curran, J.H. and Dell, S. and Mandhane, P. and Scott, J.A. and Sears, M.R. and Subbarao, P. and Takaro, T.K. and Turvey, S.E. and Wheeler, A.J. and Brauer, M.

DOI: 10.1186/1476-069X-12-48

Variable clinical outcome of ABCA3 deficiency in two siblings

Pediatric Pulmonology

Thavagnanam, S. and Cutz, E. and Manson, D. and Nogee, L.M. and Dell, S.D.

DOI: 10.1002/ppul.22698

A parent-child dyad approach to the assessment of health status and health-related quality of life in children with asthma

PharmacoEconomics

Ungar, W.J. and Boydell, K. and Dell, S. and Feldman, B.M. and Marshall, D. and Willan, A. and Wright, J.G.

DOI: 10.2165/11597890

Middle ear ventilation in children with primary ciliary dyskinesia

International Journal of Pediatric Otorhinolaryngology

Wolter, N.E. and Dell, S.D. and James, A.L. and Campisi, P.

DOI: 10.1016/j.ijporl.2012.07.011

Diffuse and interstitial lung disease and childhood rheumatologic disorders

Current Opinion in Rheumatology

Dell, S. and Cernelc-Kohan, M. and Hagood, J.S.

DOI: 10.1097/BOR.0b013e328356813e

The long-term outcomes of pediatric pleural empyema: A prospective study

Archives of Pediatrics and Adolescent Medicine

Cohen, E. and Mahant, S. and Dell, S.D. and Traubici, J. and Ragone, A. and Wadhwa, A. and Connolly, B. and Weinstein, M.

DOI: 10.1001/archpediatrics.2012.1055

Mutations of DNAH11 in patients with primary ciliary dyskinesia with normal ciliary ultrastructure

Thorax

Knowles, M.R. and Leigh, M.W. and Carson, J.L. and Davis, S.D. and Dell, S.D. and Ferkol, T.W. and Olivier, K.N. and Sagel, S.D. and Rosenfeld, M. and Burns, K.A. and Minnix, S.L. and Armstrong, M.C. and Lori, A. and Hazucha, M.J. and Loges, N.T. and Olbrich, H. and Becker-Heck, A. and Schmidts, M. and Werner, C. and Omran, H. and Zariwala, M.A.

DOI: 10.1136/thoraxjnl-2011-200301

Pulmonary involvement in the systemic inflammatory diseases of childhood

Kendig and Chernick's Disorders of the Respiratory Tract in Children

Dell, S.D. and Schneider, R.

DOI: 10.1016/B978-1-4377-1984-0.00057-7

Canadian Thoracic Society 2012 guideline update: Diagnosis and management of asthma in preschoolers, children and adults: executive summary.

Canadian respiratory journal : journal of the Canadian Thoracic Society

Lougheed, M.D. and Leniere, C. and Ducharme, F.M. and Licskai, C. and Dell, S.D. and Rowe, B.H. and FitzGerald, M. and Leigh, R. and Watson, W. and Boulet, L.P. and Canadian Thoracic Society Asthma Clinical Assemby

Canadian Thoracic Society 2012 guideline update: Diagnosis and management of asthma in preschoolers, children and adults

Canadian Respiratory Journal

Lougheed, M.D. and Lemiere, C. and Ducharme, F.M. and Licskai, C. and Dell, S.D. and Rowe, B.H. and FitzGerald, M. and Leigh, R. and Watson, W. and Boulet, L.-P.

The population attributable fraction of asthma among Canadian children

Canadian Journal of Public Health

Simons, E. and To, T. and Dell, S.

Verifying a questionnaire diagnosis of asthma in children using health claims data

BMC Pulmonary Medicine

Yang, C.L. and To, T. and Foty, R.G. and Stieb, D.M. and Dell, S.D.

DOI: 10.1186/1471-2466-11-52

Socioeconomic factors and epinephrine prescription in children with peanut allergy

Paediatrics and Child Health

Coombs, R. and Simons, E. and Foty, R.G. and Stieb, D.M. and Dell, S.D.

Skeletal muscle metabolism in cystic fibrosis and primary ciliary dyskinesia

Pediatric Research

Wells, G.D. and Wilkes, D.L. and Schneiderman, J.E. and Rayner, T. and Elmi, M. and Selvadurai, H. and Dell, S.D. and Noseworthy, M.D. and Ratjen, F. and Tein, I. and Coates, A.L.

DOI: 10.1203/PDR.0b013e3181fff35f

Diagnostic yield of nasal scrape biopsies in primary ciliary dyskinesia: A multicenter experience

Pediatric Pulmonology

Olin, J.T. and Burns, K. and Carson, J.L. and Metjian, H. and Atkinson, J.J. and Davis, S.D. and Dell, S.D. and Ferkol, T.W. and Milla, C.E. and Olivier, K.N. and Rosenfeld, M. and Baker, B. and Leigh, M.W. and Knowles, M.R. and Sagel, S.D.

DOI: 10.1002/ppul.21402

Update of respiratory tract disease in children with primary ciliary dyskinesia

Proceedings of the American Thoracic Society

Sagel, S.D. and Davis, S.D. and Campisi, P. and Dell, S.D.

DOI: 10.1513/pats.201103-024SD

Diagnostic value of nasal nitric oxide measured with non-velum closure techniques for children with primary ciliary dyskinesia

Journal of Pediatrics

Mateos-Corral, D. and Coombs, R. and Grasemann, H. and Ratjen, F. and Dell, S.D.

DOI: 10.1016/j.jpeds.2011.03.007

Evidence-based performance indicators of primary care for asthma: A modified RAND Appropriateness Method

International Journal for Quality in Health Care

Teresato and Guttmann, A. and Lougheed, M.D. and Gershon, A.S. and Dell, S.D. and Stanbrook, M.B. and Wang, C. and Mclimont, S. and Ristovska, J. and Crighton, E.J. and Fisman, D.N.

DOI: 10.1093/intqhc/mzq061

Asthma and allergic disease prevalence in a diverse sample of Toronto school children: Results from the Toronto child health evaluation questionnaire (T-cheq) study

Canadian Respiratory Journal

Dell, S.D. and Foty, R.G. and Gilbert, N.L. and Jerrett, M. and To, T. and Walter, S.D. and Stieb, D.M.

Exploring variation and predictors of residential fine particulate matter infiltration

International Journal of Environmental Research and Public Health

Clark, N.A. and Allen, R.W. and Hystad, P. and Wallace, L. and Dell, S.D. and Foty, R. and Dabek-Zlotorzynska, E. and Evans, G. and Wheeler, A.J.

DOI: 10.3390/ijerph7083211

Canadian Thoracic Society Asthma Management Continuum - 2010 Consensus Summary for children six years of age and over, and adults,Le continuum de prise en charge de l'asthme de la Socit canadienne de thoracologie - Sommaire consensuel 2010 pour les enfants de six ans et plus et les adultes

Canadian Respiratory Journal

Diane Lougheed, M. and Lemire, C. and Dell, S.D. and Ducharme, F.M. and Mark FitzGerald, J. and Leigh, R. and Licskai, C. and Rowe, B.H. and Bowie, D. and Becker, A. and Boulet, L.-P.

Predictors of universal influenza vaccination uptake in grades 1 and 2 Toronto school children: Effective vaccination strategies should not end with at risk children

Vaccine

Foty, R.G. and Guttmann, A. and Kwong, J.C. and Maaten, S. and Manuel, D. and Stieb, D.M. and Dell, S.D.

DOI: 10.1016/j.vaccine.2010.06.097

Can an evidence-based guideline reminder card improve asthma management in the emergency department?

Respiratory Medicine

To, T. and Wang, C. and Dell, S.D. and Fleming-Carroll, B. and Parkin, P. and Scolnik, D. and Ungar, W.J. and Bikangaga, P. and Petrou, C. and MacLusky, I. and Ghulmiyyah, M. and Shahsavar, A. and Zlatanovski, M. and Vasilevska-Ristovska, J. and Reisman, J.

DOI: 10.1016/j.rmed.2010.03.028

Do questions reflecting indoor air pollutant exposure from a questionnaire predict direct measure of exposure in owner-occupied houses?

International Journal of Environmental Research and Public Health

Loo, C.K.J. and Foty, R.G. and Wheeler, A.J. and Miller, J.D. and Evans, G. and Stieb, D.M. and Dell, S.D.

DOI: 10.3390/ijerph7083270

Canadian Thoracic Society Asthma Committee commentary on long-acting beta-2 agonist use for asthma in Canada

Canadian Respiratory Journal

Lougheed, M.D. and Lemiere, C. and Dell, S. and Ducharme, F. and FitzGerald, J.M. and Leigh, R. and Licskai, C. and Rowe, B.H. and Bowie, D. and Becker, A. and Boulet, L.-P.

Sputum induction in routine clinical care of children with cystic fibrosis

Journal of Pediatrics

Al-Saleh, S. and Dell, S.D. and Grasemann, H. and Yau, Y.C.W. and Waters, V. and Martin, S. and Ratjen, F.

DOI: 10.1016/j.jpeds.2010.06.001

SP-D counteracts GM-CSF-mediated increase of granuloma formation by alveolar macrophages in lysinuric protein intolerance

Orphanet Journal of Rare Diseases

Douda, D.N. and Farmakovski, N. and Dell, S. and Grasemann, H. and Palaniyar, N.

DOI: 10.1186/1750-1172-4-29

Non-tuberculous mycobacteria in children with cystic fibrosis: Isolation, prevalence, and predictors

Pediatric Pulmonology

Radhakrishnan, D.K. and Yau, Y. and Corey, M. and Richardson, S. and Chedore, P. and Jamieson, F. and Dell, S.D.

DOI: 10.1002/ppul.21106

Clinical and genetic aspects of primary ciliary dyskinesia/kartagener syndrome

Genetics in Medicine

Leigh, M.W. and Pittman, J.E. and Carson, J.L. and Ferkol, T.W. and Dell, S.D. and Davis, S.D. and Knowles, M.R. and Zariwala, M.A.

DOI: 10.1097/GIM.0b013e3181a53562

Health outcomes in low-income children with current asthma in Canada

Chronic Diseases in Canada

To, T. and Dell, S. and Tassoudji, M. and Wang, C.

An evaluation of pediatric asthma educational resources

Social Work in Health Care

Nicholas, D.B. and Dell, S.D. and Fleming-Carroll, B. and Selkirk, E.K.

DOI: 10.1080/00981380802589936

Risk Factors for Repeat Adverse Asthma Events in Children After Visiting an Emergency Department

Ambulatory Pediatrics

To, T. and Wang, C. and Dell, S. and Fleming-Carroll, B. and Parkin, P. and Scolnik, D. and Ungar, W.

DOI: 10.1016/j.ambp.2008.04.008

The burden of illness experienced by young children associated with asthma: A population-based cohort study

Journal of Asthma

To, T. and Dell, S. and Dick, P. and Cicutto, L.

DOI: 10.1080/02770900701815743

Primary ciliary dyskinesia: Myths and realities

Paediatrics and Child Health

Dell, S.D.

Diffuse lung disease in young children: Application of a novel classification scheme

American Journal of Respiratory and Critical Care Medicine

Deutsch, G.H. and Young, L.R. and Deterding, R.R. and Fan, L.L. and Dell, S.D. and Bean, J.A. and Brody, A.S. and Nogee, L.M. and Trapnell, B.C. and Langston, C. and Albright, E.A. and Askin, F.B. and Baker, P. and Chou, P.M. and Cool, C.M. and Coventry, S.C. and Cutz, E. and Davis, M.M. and Dishop, M.K. and Galambos, C. and Patterson, K. and Travis, W.D. and Wert, S.E. and White, F.V.

DOI: 10.1164/rccm.200703-393OC

Realities of expectorated sputum collection in the pediatric cystic fibrosis clinic

Archives of Pediatrics and Adolescent Medicine

Radhakrishnan, D.K. and Corey, M. and Dell, S.D.

DOI: 10.1001/archpedi.161.6.603

Congenital heart disease and other heterotaxic defects in a large cohort of patients with primary ciliary dyskinesia

Circulation

Kennedy, M.P. and Omran, H. and Leigh, M.W. and Dell, S. and Morgan, L. and Molina, P.L. and Robinson, B.V. and Minnix, S.L. and Olbrich, H. and Severin, T. and Ahrens, P. and Lange, L. and Morillas, H.N. and Noone, P.G. and Zariwala, M.A. and Knowles, M.R.

DOI: 10.1161/CIRCULATIONAHA.106.649038

Parent-reported symptoms may not be adequate to define asthma control in children

Pediatric Pulmonology

Dell, S.D. and Foty, R. and Becker, A. and Franssen, E. and Chapman, K.R.

DOI: 10.1002/ppul.20705

Persistence and remission in childhood asthma: A population-based asthma birth cohort study

Archives of Pediatrics and Adolescent Medicine

To, T. and Gershon, A. and Wang, C. and Dell, S. and Cicutto, L.

DOI: 10.1001/archpedi.161.12.1197

Massive hemoptysis in an 11-year-old girl with isolated pulmonary arteritis

Pediatric Pulmonology

Chan, E.Y. and Avcin, T. and Dell, S. and Manson, D. and Cutz, E. and Schneider, R. and Ratjen, F.

DOI: 10.1002/ppul.20527

Case verification of children with asthma in Ontario

Pediatric Allergy and Immunology

To, T. and Dell, S. and Dick, P.T. and Cicutto, L. and Harris, J.K. and MacLusky, I.B. and Tassoudji, M.

DOI: 10.1111/j.1399-3038.2005.00346.x

Pulmonary alveolar proteinosis associated with anti-GM-CSF antibodies in a child: Successful treatment with inhaled GM-CSF

Pediatric Pulmonology

Price, A. and Manson, D. and Cutz, E. and Dell, S.

DOI: 10.1002/ppul.20347

Pediatric interstitial lung disease masquerading as difficult asthma: Management dilemmas for rare lung disease in children

Canadian Respiratory Journal

Chan, E.Y. and Dell, S.D.

Obesity and asthma [2] (multiple letters)

Journal of Pediatrics

Hasan, R.A. and Nolan, B.M. and To, T. and Vydykhan, T.N. and Dell, S. and Tassoudji, M. and Harris, J.K.

DOI: 10.1016/j.jpeds.2004.11.013

Tackling paediatric asthma - The time has come

Paediatrics and Child Health

Dell, S.

Is obesity associated with asthma in young children?

Journal of Pediatrics

To, T. and Vydykhan, T.N. and Dell, S. and Tassoudji, M. and Harris, J.K.

DOI: 10.1016/j.jpeds.2003.09.047

Breastfeeding and asthma in young children: Findings from a population-based study

Archives of Pediatrics and Adolescent Medicine

Dell, S. and To, T.

Childhood asthma admissions: Determinants of short stay

Pediatric Allergy and Immunology

Dell, S.D.M. and Parkin, P.C. and Macarthur, C.

DOI: 10.1034/j.1399-3038.2001.0s079.x

Genetic Diseases of Mucociliary Clearance Consortium (GDMCC)

I am one of 8 principal investigators in this NIH funded collaboration which studies the genetic causes, disease characteristics, clincial management and health outcomes of primary ciliary dyskinesia (PCD) and supporative lung disease in children.

PCD Registry

This project sponsored by the PCD Foundation is currently supporting 4 pilot sites to develop a longitudinal disease registry for research and health outcomes reporting of patients with PCD.

Cellular mechanisms underlying sensory motile ciliopathies

This CIHR-funded project is studying why some patients with a form of genetic blindness called RPGR also develop PCD lung disease.

Grants

Apr 2020 – Mar 2021 - Co-Investigator. FActors of Mothers and Infants in Longitudinal Years (FAMILY)- A maternal and child birth cohort with babies identified from three Ontario existing pediatric cohorts and linked with health administrative data to create a birth cohort of infants and their siblings and mothers to study prenatal, postnatal and early childhood factors associated with maternal and child health and developmental outcomes. Canadian Institutes of Health Research (CIHR) Operating Grant- Data Analysis. PI - To T, Borkhoff C. Co-applicants - Anderson L, Birken C, Dlle S, Guttman B, Janus M, Maguire J, Moraes T, Parkin P, Subbarao P, Van Dam A. $75,000 CAD. Non-industry sponsored.

Aug 2019-Jul 2024 - Principal Investigator. Genetic Disorders of Mucociliary Clearance. National Institute of Health (NCATS/NHLBI) 2U54HL096458-16. Nominated Principal investigator - Davis S. Co-Principal Investigators - Dell S, Ferkol T, Knowles, M, Rosenfeld M.. $6,249,996.000 USD ($219,540 USD to Dell). Non-Industry Sponsored. I am PI of the Career Enhancement Core Subproject, Subaward Award #5116143.

Apr 2019 – Mar 2023 - Principal Investigator. The cellular mechanisms underlying sensory motile ciliopathies. Canadian Institutes of Health Research (CIHR). PI - Heon E., Mennella V. $604,351 CAD. Non-industry sponsored. (Promoted form co-I to PI due to Mennella moving to UK).

Sep 2016-Apr 2021 - Principal Investigator. Outdoor Pollution Exposure and Risk Assessment - OPERA – Risk Assessment – A new paradigm for Evidence Based Decision Making in Climate and Air Quality Management. Health Canada. Nominated Principal Investigator - Rick Burnett. Co-Principal Investigators - Chen H, Dell S, Lavigne E, Stieb S, To T, Tjepkema M, Weichenthal S. $2,380,100 CAD ($470,000 CAD to The Hospital for Sick Children site). Non-Industry Sponsored.

Aug 2014-Jul 2019 - Principal Investigator. Genetic Disorder of Mucociliary Clearance. National Institute of Health (NIH). Nominated Principal investigator - Knowles, M. Co-Principal Investigators - Davis S, Fordham L, Leigh M, Dell S, Ferkol T, Krischer J, Milla C, Sagel S, Rosenfeld M, McShane P. $6,249,996.000 USD ($219,540 USD to Toronto site) Non-Industry Sponsored.

July 2018-June 2019 - Principal Investigator. Unbiased and automated diagnosis of ciliopathies by super-resolution microscopy and machine learning. HSBC Bank Canada Catalyst Research Grant, SickKids Foundation. Co-applicants - Anna Goldberg, Richard Hegele, Vito Mennella. $50,000 CAD. Non-industry sponsored.

Apr 2018 – Mar 2019 - Co-Investigator. The cellular mechanisms underlying sensory motile ciliopathies. Canadian Institutes of Health Research (CIHR). PI - Mennella V, Co-PI Elise Heon. $650,250 CAD. Non-industry sponsored. (Terminated early due to Mennella moving to UK).

Jan 2018 – Jan 2020 - Principal Investigator. Development of diagnostic toolbox to diagnose complex PCD cases. ATS Foundation/PCDF Research Grant. PI - Vito Mennella. $80,000 USD. Non-industry sponsored. Declined due to PI (VM) leaving SickKids.

Oct 2017 – June 2018 - Co-Investigator. Sensory Cilia Mutations Affecting Motile Cilia in Ciliopathy Disorders. Canadian Institutes of Health Research (CIHR). PI - Mennella V. Co-investigator - Heon E. $75,000 CAD. Non-industry sponsored.

Jan 2018 – Dec 2018 - Co-Principal Investigator. The prevalence and morbidity of ciliary genetic mutations in patients with specific congenital heart disease phenotypes – a retrospective cohort study. PI - Pisesky A, Ghandourah H, Dell S, Mennella V, Mital S, Nield LE. The Labatt Family Heart Centre. $10,000 CAD. Non-industry sponsored.

Jul 2016-Dec 2018 - Principal Investigator. A Phase 2a, Randomized, Double-blind, Placebo-controlled, Incomplete Block Crossover Study to Evaluate the Safety and Efficacy of VX-371 Solution for Inhalation in Subjects with Primary Ciliary Dyskinesia. Short title - CLEAN-PCD - Clearing Lungs with ENac Inhibition in Primary Ciliary Dyskinesia. Parion Sciences Incorporated. PS-G202. Co-Investigators - Ratjen F, Sweezey N. $217,000 CAD. Industry Sponsored Contract.

Jul 2016-Jul 2017 - Principal Investigator. Primary Ciliary Dyskinesia diagnosis by Super Resolution Microscopy. Ontario Lung Association, Grant-in-aid competition. Principal Investigator - Mennella, Vito. Collaborator - Moraes, Theo. $49,939 CAD. Non-Industry Sponsored.

Honours & Awards

2018 - American Thoracic Society Fellow (ATSF), The ATS Fellow designation is a mark of distinction, conferring recognition on members for their accomplishments, dedication and contributions to the Society as well as to the fields of pulmonary, critical care, and sleep medicine.

2016 - American Thoracic Society Clinician Educator Award, American Thoracic Society Pediatric Assembly, San Francisco, CA, USA. This award is presented annually to one ATS member who demonstrates outstanding and innovative clinical and teaching abilities through a nomination and peer reviewed process. Total Amount $1000.

2016 (Feb-Aug) - Visiting Scholar, Clinical Epidemiology Program, Sydney School of Public Health, Faculty of Medicine, University of Sydney, Sydney, NSW, Australia.

2013 - Claus Wirsig Humanitarian Award, SickKids Foundation, Toronto, ON, Canada. This Award is presented annually to one SickKids health professional or support staff who has consistently demonstrated qualities of compassion and humanitarianism in providing care to patients and their families and also makes a significant contribution to the teaching of these values to their peers. Candidate selection is through a nomination and peer reviewed process.

2001 - The Children's Hospital Foundation Award, Resident, The Children’s Hospital, Winnipeg, Manitoba, Canada. First prize for the Canada wide 13th Annual Pediatric Resident and Fellows Research Competition.

1997 - Restracomp Fellowship Student, Sick Kids Research Institute, Toronto, ON, Canada. Salary Support for epidemiology training (Sept 1997-1999).

1987-89 - Dr. F.J. Colling O.B.E. Memorial Scholarship, Student, University of Toronto, Toronto, ON, Canada. Overall academic achievement (top 10 standing) in Medical School.

1988 - Ronald S. Saddington Prize in Pathology, Student, University of Toronto, Toronto, ON, Canada. Academic Achievement in Pathology.

1982 - George and Nora Elwin Entrance Scholarship, Student, McMaster University, Hamilton, ON, Canada. Entrance Scholarship Award.

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